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題 名 | Primary Renal Angiosarcoma: A Case Report=原發性腎臟血管肉瘤:病例報告及文獻回顧 |
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作 者 | 阮春榮; 吳清俊; 薛俊仁; 蕭海松; 劉昌憲; 韓鴻志; 范洪春; 于大雄; | 書刊名 | 中華放射線醫學雜誌 |
卷 期 | 25:2 2000.04[民89.04] |
頁 次 | 頁87-90 |
分類號 | 416.273 |
關鍵詞 | 腎臟腫瘤電腦斷層攝影; 腎臟腫瘤血管攝影; 血管肉瘤; Kidney neoplasms CT; Kidney neoplasms angiography; Angiosarcoma; |
語 文 | 英文(English) |
中文摘要 | 原發性腎臟血管肉瘤是一種高度惡性且預後極差的血管腫瘤。我們報告一位罹患原發性腎臟血管肉瘤之八十一歲女性。臨床上病患僅表現出無痛性明顯的血尿。此腫瘤卻在電腦斷層上呈現不規則的邊緣及壞死,與典型的腎臟細胞瘤不相同。血管攝影檢顯示有少許的腫瘤新生血管及腫瘤濃染,排除了腎臟發炎的可能性。最後之診斷仍需依賴病理切片。除了腎臟切除手術外,病患並接受放射治療。然而,六個月後之超音波及電腦斷層追蹤發現肝臟有轉移之病灶。經過保守性之化學治療之後,病患仍因肝衰竭引發肝腦病變而於術後9個月死亡。我們回顧文獻發現本病例是目前所有報告中年齡最大的一位。 |
英文摘要 | Primary renal angiosarcoma is a high-grade malignant vascular tumor with a dismal prognosis. An 81-year-old woman with a primary angiosarcoma of the left kidney presented with a 3-month history of painless gross hematuria. On contrast-enhanced CT scans, the tumor was more infiltrative than that typically seen in renal cell carcinoma. Angiography, which was performed in order to differentiate a malignant tumor from an inflammatory mass, revealed a small number of tumor vessels and tumor stain. In addition to a radical nephrectomy, the patient received radiotherapy on the left renal fossa with a total of 4.35 Gy. Unfortunately, a follow-up sonogram revealed diffuse liver metastasis 6 months after surgery. Palliative chemotherapy including Ifosphamide and Mesna was given. However, hepatic failure complicated with hepatoencephalopathy developed during the 3rd course of chemotherapy. The patient died 9 months after nephrectomy. To our knowledge, this is the oldest reported patient with primary renal angiosarcoma. |
本系統中英文摘要資訊取自各篇刊載內容。