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題 名 | Light and Electron Microscopic Studies of the Variant Type of Reis-Bucklers' Corneal Dystrophy--Case Report=雷斯--巴克角膜失養症變異型之顯微研究--病例報告 |
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作 者 | 郭乃文; 陳俊良; 許淑娟; 陳昌文; 王志生; 張倩毓; | 書刊名 | 中華民國眼科醫學會雜誌 |
卷 期 | 37:1 1998.03[民87.03] |
頁 次 | 頁43-48 |
分類號 | 416.711 |
關鍵詞 | 雷斯巴克角膜失養症; Corneal dystrophy; Reis-Bucklers' dystrophy; Thiel-Behnke's dystrophy; Rod-shaped bodies; Curly fibers; |
語 文 | 英文(English) |
中文摘要 | 雷斯-巴克(Reis-Bucklers')角膜失養症是一種影響到角膜表皮的基質細胞, Bowman氏層,基質前層的一種角膜失養症。而其變異型Thiel-Behnke's失養症與其有共同的 一些特色:反覆性的表皮破損及晚期時視力的喪失。本研究側重於一有家族病史的四十六歲男 子經診斷為Thiel-Behnke's失養症的角膜前部顯微結構。構造中發現多處表皮基膜的缺乏、 Bowman氏層的破壞、及位於表皮基膜與Bowman氐層間典型的“peculiar-curly"纖維的沉積。 |
英文摘要 | Reis-Bucklers corneal dystrophy is a type of anterior corneal dystrophy involving the Bowman's membrane, anteior stroma, and basal cells of the corneal epithelium. Despite of the similar clinical characteristics: recurrent epithelial erosion, and progressive visual loss in a later stage; the variant, Thiel-Behnke's dystrophy, had the typical electron microscopic findings. The literature presents the ultrastructural characteristics of pithelium, Bowman's layer, and anterior stroma from the corneal tissue of a 46 years old adult with the diagnosis of Thiel-Behnke's dystrophy in an affected family of three generations. The tissue reveals absence of the epithelial basement membrane in many areas, destruction of Bowman's layer, and areas of patchy deposition of characteristic "peculiar curly" filaments between a distorted epithelial basal lamina and Bowman's layer. |
本系統中英文摘要資訊取自各篇刊載內容。