查詢結果分析
來源資料
相關文獻
- Acquired Hypothalamus Secretory Dysfunction with Isolated Luteinizing Hormone Deficiency--A Case Report
- Hypothalamic Juvenile Pilocytic Astrocytoma Presenting with Intracerebral Hemorrhage
- Hypothalamic Dysfunction in Acute Head-Injured Patients with Stress Ulcer
- 天麻活性成分對位羥基苯醇改善學習記憶作用與下視丘-腦下垂體-腎上腺軸之關係
- Adenosine對於大白鼠攝食行為及下丘中神經元活性之影響
- An Unusual Concomitant Tremor and Myoclonus after a Contralateral Infarct at Thalamus and Subthalamic Nucleus
- Effects of Adrenergic Antagonists on LH Surge in Short-Term Ovariectomized-Steroids-Primed Rats
- Human Progesterone Receptor Shows Differential Sensitivity to Carboxyl Group Modifying Agents When Bound to Agonist and Antagonist Ligands
- 腦部超音波下,基底核和下視丘處線狀影像增強對早產兒神經發展預後的影響
- 醣皮素與醫原性庫欣氏症候群
頁籤選單縮合
題 名 | Acquired Hypothalamus Secretory Dysfunction with Isolated Luteinizing Hormone Deficiency--A Case Report=後天性下視丘分泌功能異常合併單純黃體激素缺乏症--病例報告 |
---|---|
作 者 | 謝政興; 黃天祥; 勞漢信; 林明中; | 書刊名 | 中華民國泌尿科醫學會雜誌 |
卷 期 | 9:1 1998.03[民87.03] |
頁 次 | 頁36-40 |
分類號 | 415.8616 |
關鍵詞 | 下視丘; 黃體激素; 柯羅米芬; Hypothalamus; Luteinizing hormone; Clomiphene; |
語 文 | 英文(English) |
中文摘要 | 單純黃體激素缺乏症經常是先天性,且具有以下特徵:(一)類宦官表徵,兩側睪 丸略小(二)睪丸有精子生成能力,但缺乏萊狄什氏細胞(三)睪丸對於人類胎盤絨毛性激 素的刺激反應正常。本文報告一位34歲男性病人結婚七年,太太曾一度懷孕,後來因故要 中止懷孕,實施人工流產,之後六年未曾懷孕;身體健康且性生活正常,直到三年前,性慾 開始降低性功能異常。除了左側精索靜脈曲張及兩側睪丸略小外,身體理學檢查正常。睪丸 活體組織切片可發現睪丸有活躍的精子生成能,但萊狄什氏細胞數目明顯減少。荷爾蒙分析 顯示血清濾泡刺激激素及泌乳激素濃度正常,黃體激素及睪固酮濃度低於正常值。頭部電腦 斷層攝影檢查發現腦下垂體發育不全,但無可見的腫瘤。對於性腺釋放激素,甲狀腺釋放激 素及胰島素耐性試驗反應正常。柯羅米芬(Clomiphene)試驗反應亦正常,荷爾蒙波動分析沒 有觀察到黃體激素的波動,並且黃體激素濃度持續低於正常值:濾泡刺激激素的波動分析則 是正常。發生於本例的單純黃體激素缺乏症是後天性的,產生病變的部位可能在下視丘,其 分泌功能異常,無法正常加強性腺釋放激素的分泌。柯羅米芬(Clomiphene)是一種可以刺激 下視丘的化合物,這位病人在服用柯羅米芬一個月後,臨床上反應良好,性慾及性功能恢復 正常。 |
英文摘要 | A 34-year-old male was seen for evaluation of a barren marriage of 7 years. He had been healthy with a normal sexual life until 3 years ago when the libido decreased with defective intercourse. He had testes of subnormal size and preserved spermatogenesis with mild decrease in the number of the Leydig cells. Hormond assay revealed FSH 10.9 mIU/ml, LH 0.6 mlU/ml and testosterone 0.94 ng/ml. Normal response was demonstrated in GnRH test, TRH test and ITT test. Pulse study by determining basal FSH and LH every 10 minutes revealed no observable LH pulse and sustained low level of LH within 8 hours. He responded well to clomiphene administration clinically and biochemically, and regained sexual drive and function after clomiphene 100 mg daily was administered for one month. The manifestation corresponded to the entity characterized by fertile eunuch syndrome, which was generally believed to be congenital and a less severe form of idiopathic hypogonadotropic hypogonaddism. However, the hypothalamus secretory dysfunction with isolated LH deficiency in this case was characterized as acquired. |
本系統中英文摘要資訊取自各篇刊載內容。