頁籤選單縮合
| 題 名 | G症候群併喉裂--病例報告=G Syndrome Associated with Laryngeal Cleft--Case Report |
|---|---|
| 作 者 | 楊政謙; 李國森; 王麟殿; 徐銘燦; | 書刊名 | 中華民國耳鼻喉科醫學會雜誌 |
| 卷 期 | 33:1 1998.02[民87.02] |
| 頁 次 | 頁92-96 |
| 分類號 | 417.5688 |
| 關鍵詞 | 喉裂; 喉氣管食道裂; G症候群; Laryngeal cleft; Laryngotracheoesophageal cleft; G syndrome; |
| 語 文 | 中文(Chinese) |
| 中文摘要 | 喉裂或喉氣管食道裂及 G 症候群為一種罕見的先天性異常。G 症候群如果伴有喉 裂或喉氣管食道裂則常使治療更困難甚至因呼吸道的併發症而造成死亡,即使是沒有併發其 他異常的喉裂或喉氣管食道裂在診斷及治療上均是一項挑戰。 馬偕紀念醫院耳鼻喉科於 1996 年 11 月經歷 1 例足月產的男性新生兒,臨床表現有眼距過長、唇裂、顎裂及尿道下 裂等先天異常,因為有喘鳴、餵食困難、生長遲滯且有反覆吸入性肺炎必須持續氣管內插管 , 由臨床症狀及纖維內視鏡檢查診斷為 G 症候群併有喉裂異常的病例,我們以內視鏡顯微 手術的方法修補喉裂。病人手術後喘鳴、胸凹及嗆咳的現象改善,餵食量及體重均增加並且 持續門診追蹤治療。 |
| 英文摘要 | Laryngeal cleft and laryngotracheoesophageal clefts or G syndrome are rare congenital anomalies. Diagnosis of laryngeal cleft or laryngotracheoesophageal cleft is not easy especially when they are associated with other anomalies. G syndrome is difficult to manage if it is complicated with laryngeal cleft or laryngotracheoesophageal cleft due to airway complications. In November 1996 we encountered a 42 days old male neonate who has hypertelorism, cleft lip, cleft palate and hypospadia at birth. Respiratory stridor, feeding difficulty, growth retardation, and recurrent aspiration developed thereafter. He received prologing intubation for relief of respiratory distress. Fiberoptic endoscopy revealed larygeal cleft extending to the cricoid level. Primary repair of the cleft was successful using microscopic suturing technique under direct laryngoscopy. The symptoms and signs of the upper aerodigestive tract improved after operation. The patient follows up at out patient department regularly. |
本系統中英文摘要資訊取自各篇刊載內容。