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題 名 | T-cell Lymphoma Involved Liver and Terminal Ileum Complicated with Reactive Hemophagocytic Syndrome: Report of a Case=T細胞淋巴瘤侵犯肝臟和末端迴腸合併血球吞噬症候群:一病例報告 |
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作 者 | 曾文怡; 黎國洪; 羅錦河; 巫宏博; 蔡正中; 曾暉華; | 書刊名 | 中華民國消化系醫學雜誌 |
卷 期 | 14:3 1997.09[民86.09] |
頁 次 | 頁27-32 |
分類號 | 415.6 |
關鍵詞 | 肝臟; T細胞淋巴瘤; 血球吞噬症候群; 末端迴腸; Liver; Reactive hemophagocytic syndrome; T-cell lymphoma; Terminal ileum; |
語 文 | 英文(English) |
中文摘要 | 血球吞噬症候群是一種罕見之疾病,一般常以發燒、血球減少、凝血異常、肝脾 腫大,以及全身性組織細胞球(histiocyte)增生且吞噬血球。此病常併發於一些潛在性疾病, 例如淋巴瘤、白血病,以及各種感染症等。 今報告之病例為26歲男性,主訴發燒、發冷、及皮膚變黃。入院檢查發現有血球減少、 凝血異常、及肝脾腫大。肝切片發現Kupffer細胞有明顯吞噬紅血球之現象。病人接受積極 之免疫抑制治療,不幸續發末端迴腸破裂;雖經手術治療(切除之迴腸發現淋巴瘤侵犯), 但最後病人仍死於術後之併發症。病理解剖證實為一T細胞淋巴瘤侵犯肝臟和末端迴腸合 併血球吞噬症候群。 |
英文摘要 | Reactive hemophagocytic syndrome (RHS) is a disorder characterized by systemic proliferation of benign hemophagocytic histiocytes, fever, cytopenia, coagulopathy and hepatosplenomegaly. It has been associated with many underlying disorders including leukemia, lymphoma, and many kinds of infection. We report a case of a 26-year-old make suffering from fever, chills, jaundice, hepatosplenomegaly, cytopenia, and coagulopathy. Liver biopsy revealed many Kupffer cells with phagocytosis of erythrocytes. He received aggressive immunosuppressive therapy under the diagnosis of RHS, but he died from complications of underlying malignant lymphoma. |
本系統中英文摘要資訊取自各篇刊載內容。