頁籤選單縮合
題 名 | Bilateral Multicystic Kidney Dysplasia in a Fetus with Neonatal Pulmonary Hyaline Membrane Disease:A Case Report=嬰兒兩側多囊性腎臟發育不良合併肺透明膜疾病:一例報告 |
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作 者 | 廖建添; 謝俊賢; 張榮州; 張旭陽; | 書刊名 | 長庚醫學 |
卷 期 | 20:4 1997.12[民86.12] |
頁 次 | 頁335-339 |
分類號 | 417.574 |
關鍵詞 | 多囊性腎臟發育不良; 肺透明膜疾病; Multicystic dysplastic kidney; Hyaline membrane disease; |
語 文 | 英文(English) |
中文摘要 | 多囊性腎臟發育不良是最常見的新生兒腎臟腫瘤及腹部腫瘤,它可以是單側性或 是兩側性,發生率約為五千分之一至萬分之一,單側性約佔百分之七十五,男女比率約為二 比一,單側性通常沒有症狀會自然地恢復,但兩側性常常是致死性的。近來醫學進步,超音 波解析度的改進,提高了產前胎兒異常的診斷,給予胎兒父母更多的醫療諮詢,裨使對於患 有此症的胎兒有良好之處理及治療。多囊性腎臟發育不良應做詳盡的嬰兒心電圖以發現相關 之心臟病,並照會小兒泌尿科作進一步評估及處理,總之,在懷孕時發現多囊性腎臟發育不 良時須有醫療團隊來處理,包括高危險妊娠科、小兒泌尿科、新生兒科、細胞遺傳學科等醫 師來共同努力。 |
英文摘要 | Multicystic kidney disease is the most common cause of neonatal renal mass and either the most or second most common neonatal abdominal mass. This disease is a congenital dysplasia of the kidney characterized by large nonhomogeneous dilations of the collecting tubules. It may occur unilaterally or bilaterally, and the incidence is about 1 out of 5,000 to 10,000 births. Severe bilateral defects are lethal. Partial dysplastic involvement of both kidneys eventually leads to renal function impairment. This is a case of bilateral multicystic kidney dysplasia diagnosed prenatally at 34 weeks of gestation. Hyaline membrane disease was found in both lungs after delivery. The antenatal diagnostic criteria for multicystic kidney disease and treatment after diagnosis are also discussed. |
本系統中英文摘要資訊取自各篇刊載內容。