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題 名 | Long QT Syndrome in Children=兒童的QT延長症侯群 |
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作 者 | 吳俊明; 王玠能; 林嘉相; 李紋麗; 吳美環; | 書刊名 | 中華民國小兒科醫學會雜誌 |
卷 期 | 38:3 民86.05-06 |
頁 次 | 頁213-217+244 |
分類號 | 417.522 |
關鍵詞 | Torsade點; 心室頻脈; 瘁死; 房室間傳導阻斷; Torsades de pointes; Long QT syndrome; Ventricular tachycardia; Sudden death; Atrioventricular block; |
語 文 | 英文(English) |
英文摘要 | Long QT syndrome is a disease that can cause syncope, seizures and sudden death. From June 1990 to June 1996, 11 children (male/female: 7/4; ages: 1 days-13 years with a median of 5.4 years) from different families were found to have long QT syndrome. Their corrected QT intervals (QTc) were 0.46-0.59 sec (median: 0.53 sec). All patients had normal hearing. One patient had Marfan syndrome with mitral valve prolapse. The presentation symptoms were: sudden death (2), seizures (6) and syncope (3). Their electrocardiogram abnormalities included: torades de pointes (7), sinus bradycardia (4), T wave abnormalites (4) , monomorphic ventricular tachycardia (2) and congenital complete atrioventricular block (1). All patients were treated with β -blockers and one had pacemaker implantation. In a follow-up period of 0.5-6 year, 6 were symptom free, 1 died of ventricular tachycardia and 2 had recurrent syncope. |
本系統中英文摘要資訊取自各篇刊載內容。