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題 名 | Angiotropic Lymphoma Manifesting as a Solitary Adrenal Tumor in a Case of Ankylosing Spondylitis=僵直性脊椎炎病患併發以單側腎上腺腫瘤為表現之親血管性淋巴瘤 |
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作 者 | 高志平; 邱昌芳; 劉顯敏; 徐會棋; 何照洪; 周永強; | 書刊名 | 中華醫學雜誌 |
卷 期 | 63:1 2000.01[民89.01] |
頁 次 | 頁62-65 |
分類號 | 415.6 |
關鍵詞 | 腎上腺腫瘤; 親血管性淋巴瘤; 僵直性脊椎炎; 化學治療; Adrenal tumor; Angiotropic lymphoma; Ankylosing spondylitis; Chemotherapy; |
語 文 | 英文(English) |
中文摘要 | 親血管性淋巴瘤是極為罕見的,其特徵表現為大型淋巴瘤細胞聚積在被侵犯器官 的血管內。這是一種全身性病變,常有發燒、皮膚病變及神經系統症狀等臨床表現。我們在 此報告一 69 歲男性新病例。該病患的臨床表現是發燒、體重減輕,同時在左側腎上腺發現 有一腫瘤。在進行手術切除後,病理報告證實了該腫瘤為一親血管性淋巴瘤。在輔以化學治 療後,病患情況良好,至今無病存活已達 44 個月。此外,該病患在此次淋巴瘤診斷之前已 有 10 年僵直性脊椎炎病史。 回顧文獻報導,這是第 1 例僵直性脊椎炎與親血管性淋巴瘤 相關的報告, 也是第 2 例僅以單側腎上腺腫瘤表現而未有侵犯身體其它部位的親血管性淋 巴瘤報告。 |
英文摘要 | Angiotropic lymphoma is an extremely rare disease characterized by intravascular accumulation of large neoplastic lymphocytes, with the clinical manifestations of fever, skin lesions and neurologic deficits. We report a patient who developed angiotropic lymphoma after a 10-year history of ankylosing spondylitis. The clinical disease manifested as a unilateral, solitary adrenal tumor, fever and body weight loss. The fever subsided after surgical removal of the adrenal tumor. Systemic chemotherapy was administered postoperatively. The patient was leading an uneventful life 44 months after the initial diagnosis. To our knowledge, this is the first case of angiotropic lymphoma associated with ankylosing spondylitis. It is also the second reported case manifesting with a unilateral solitary adrenal tumor without systemic involvement. |
本系統中英文摘要資訊取自各篇刊載內容。