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題 名 | Primary Aldosteronism: 13 Cases Analysis=原發性醛固酮症:13病例分析 |
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作 者 | 廖文魁; 林石化; 吳篤安; 傅茂祖; | 書刊名 | 醫學研究 |
卷 期 | 17:2 1996.09[民85.09] |
頁 次 | 頁123-130 |
分類號 | 415.934 |
關鍵詞 | 血漿醛固酮濃度; 血漿腎素活性; 腎上腺皮質腺瘤; 腎上腺皮質增生; 原發性腎上腺皮質結節增生; Plasma aldosterone concentration; PAC; Plasma renin activity; PRA; Aldosterone-producing adenoma; APA; Idiopathic hyperaldosteronism; IHA; Primary adrenal hyperplasia; PAH; |
語 文 | 英文(English) |
英文摘要 | Thirteen cases of primary aldosteronism from June, 1986 to June, 1992 were studied. The presenting symptoms were mainly muscle weakness (12/13), headache (11/13), dizziness (8/13), polyuria (6/13), and syncope (2/13). The most frequent sign in all cases was hypertension (mean 3 years), flaccid paralysis in three cases, and recent CVA, cardiomegaly in one case. Twelve cases had serum potassium levels less than 3.0 mEq/L (2.5±0.3 mEq/L). Nine cases had serum sodium levels more than 145 mEq/L (146.9±3.3 mEq/L). Daily urinary K excretion more than 30 mEq were found in 12 cases (44.3±16.2 mEq/day). All cases had increased PAC (765.7±277.9 pg/ml) and decreased PRA. The ratio of PAC to PRA were greater than 30 in all cases. Five cases received saline infusion test, and all revealed non-suppressible PAC (more than 85 pg/ml). Further investigations included abdominal CT scan (13/13), posture test (6/13), and adrenal vein sampling (7/13). Nine cases of aldosterone-producing adenoma, and 4 cases of idiopathic hyperaldosteronism were diagnosed. All of 9 cases received unilateral adrenalectomy and 8 cases were proved as cortical adenoma and one case as nodular hyperplasia by the pathologic findings. The hypertension and hypokalemia were cured within 3 months in all APA cases receiving unilateral adrenalectomy. Four cases of idiopathic hyperaldosteronism received spironolactone treatment and responded well except one case of presumptive primary adrenal hyperplasia with paradoxical fall of plasma aldosterone concentration by posture test and diuretics test like a form of an adenoma. We own that abdominal CT scan (13/13) can provide a reliable method for identification of tumor (diagnostic accuracy 92.3%). Besides, the simple posture test (6/13) is a very useful adjunctive method (diagnostic accuracy 83.3%), and may diagnose primary adrenal hyperplasia which can be cured by surgery. Adrenal vein sampling (7/13), which is renal vein sampling actually in our cases with diagnostic accuracy 71.4%, can be performed for the localization of tumor and the identification of unilateral or bilateral disease when the distinction was inclusive by the CT scan and posture test. |
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