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題 名 | 水疱型全身性紅斑性狼瘡=Bullous Systemic Lupus Erythematosus |
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作 者 | 蔡東家; 許乃仁; 宗天一; 陳自強; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 17:3 1999.09[民88.09] |
頁 次 | 頁254-262 |
分類號 | 415.67 |
關鍵詞 | 水疱; 全身性紅斑性狼瘡; Systemic lupus erythematosus; Bullous; |
語 文 | 中文(Chinese) |
中文摘要 | 一位22歲女性,罹患水�秤f灶有兩個多月。水�秘o於臉部、頸部、兩側腋下、四 肢及軀幹。皮膚組織病理顯示有表皮下水�砲穻芋C水�砟漲陶畾眵y、嗜伊紅性白血球、多形 核白血球及細胞核碎片。水�祚ヵu皮有明顯嗜中性白血球浸潤。直接免疫螢光檢查顯示在基 底膜區 IgG、IgM、IgA 及 C3 呈帶狀沉積。 以 1.0M 氯化鈉溶液浸泡處理後裂開的病灶旁 皮膚做直接免疫螢光檢查顯示 IgG、IgM、IgM、IgA 及 C3 皆於真皮側。以正常人皮膚作間 接免疫螢光檢查及以 1.0M 氯化鈉溶液浸泡處理後裂開的正常皮膚做間接免疫螢光檢查兩者 皆呈陰性反應。 皮膚特徵、腎臟切片符合狼瘡腎炎第四級 (lupus nephritis, class Ⅳ ) 、抗核抗體陽性、肺部有肺泡出血、蛋白尿及淋巴球減少,符合全身性紅斑性狼瘡診斷標準 。本文在此報告此一水�神洛�身性紅斑性狼瘡病例併回顧相關文獻。 |
英文摘要 | A 22-year-old female had developed vesiculobullous eruption for more than two months. The lesions were noted over the face, neck, axillae, four extremities and turnk. Histopathological examination of the vesicular lesions showed subepidermal blister formation which contained mononuclear cells, eosinophils, polymorphonuclear neutrophils, and nuclear dusts. In the periphery of the blister, neutrophils was predominantly noted in the dermis. Direct immunofluorescence (DIF) study showed linear deposition of IgG, IgM, IgA and IgG, IgM, IgA and C3 at the dermal side. Indirect immunofluorescence (Ⅱ F) on normal human skin with or without 1.0 M NaCl-split method showed negative results. Skin manifestations, renal biopsy (compatible with lupus nephritis class Ⅳ ), antinuclear antibody (ANA), alveolar hemorrhage of the lung, proteinuria and lymphocytopenia fulfilled the diagnostic criteria of SLE. We hereby report a case of bullous systemic lupus erythematosus and review the literature. |
本系統中英文摘要資訊取自各篇刊載內容。