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題 名 | An Epidemiological Study of Lip and Palate Cleft in Taiwan: Prevalence Trend and Familial Clustering=臺灣地區唇顎裂之流行病學研究--盛行率趨勢及家族聚集現象 |
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作 者 | 蕭正光; 陳建仁; 李明亮; | 書刊名 | 慈濟醫學 |
卷 期 | 7:2 1995.06[民84.06] |
頁 次 | 頁89-95 |
分類號 | 416.413 |
關鍵詞 | 唇顎裂; 盛行率趨勢; 家族聚集; Lip and palate cleft; Prevalence trend; Familial clustering; |
語 文 | 英文(English) |
中文摘要 | 本研究的目的是估計台灣地區唇顎裂之出生盛行率,以及其家族聚集情 形。本研究分析I98C至1982年,衛生署保健處所報告的130,821位新生兒,以及I990 至1992年,87,747位新生兒,發現這IS年期間唇顎裂並無明顯的變化趨勢。唇裂 合併Z不合併顎裂之出生盛行率為每十人I.匕,單純顎裂為每十人0.66。約15 叨之唇顎裂新生兒之出生體重低於2500e,比台灣地區低體重新生兒之平均盛行 率高出2倍。本研究亦訪視136位唇裂合併/不合併顎裂患者,其中有18位親屬(9.55) 亦為病例,這18位病例親屬有17位和指標病例罹患同型之唇顎裂,僅一位罹患單 純顎裂,一等親親屬較一般族群危險性高10倍以上,而二等親及三等親親屬則比 一般族群危險性高2至3倍。(慈濟醫學 1995;7:89-95) |
英文摘要 | This study was carried out to estimate the birth prevalence of lip and palate cleft in Taiwanand to explore its familial clustering. In a survey of 130,821 births during 1980 to 1982 and 87,747births during 1990 to 1992, the birth prevalence of cleft lip with or without cleft palate (CIVP)and isolated cleft palate (CP) show no significant change during the 13 years period. The birthprevalence of CUP and of CP was found to be 1.12 and 0.47 per 1,000, respectively. The sex ratio(male to female) varied between the different types of clefts: CUP had a sex ratio of 1.38 andCP had a ratio of 0.66. The prevalence of birthweight under 2500g for cleft infants was 15.3which was more than twice higher than the average prevalence of low birthweight in Taiwan. Although only 9.55 of 136 intereviewed CL/P index cases had a family history of cleft, the frequency of clefts in the relatives was in excess of that for the general population. Among the 18affected relatives of CL/P index cases, only one was affected with isolated cleft palate and theothers with CUP. (Tzu Chi Med J 1995; 7: 89-95) |
本系統中英文摘要資訊取自各篇刊載內容。