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題 名 | Ptosis Surgery on Chronic Myasthenia Gravis=重症肌無力在慢性穩定狀態時的眼瞼下垂手術 |
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作 者 | 陳宏任; 翁林仲; 周介仁; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 16:2 2000.02[民89.02] |
頁 次 | 頁95-99 |
分類號 | 416.703 |
關鍵詞 | 重症肌無力; 眼瞼下垂手術; Myasthenia gravis; Strabismus; Ptosis; |
語 文 | 英文(English) |
中文摘要 | 本篇報告三例早發性的重症肌無力病例,其臨床上都有眼瞼下垂、複視、輕度到 中度非共慟性外斜視,對 Neostigmine 檢查呈陽性反應和顏面肌、口咽肌變弱。 追蹤時間 為五到九年平均為七年,並在最近兩年的追蹤當中,呈現對口服 Pyridostigmine 與類固醇 治療近乎無效。其眼皮下垂與外斜視呈慢性穩定狀態。這三個病例,其眼球運動,最後在各 個方向都有明顯限制,幾乎呈現僵直且眼瞼下垂。本篇報告探討其臨床上的罕見狀態,以及 在肌電圖與病理上的發現。並為這三例進行 Frontalis suspension 手術,改善其眼瞼下垂 ,對其中一中度外斜視病例進行可調整性斜視手術治療其斜視,在手術後都超過一年半的追 蹤當中,其療效相當良好。 |
英文摘要 | We report three cases of long-standing, early onset myasthenia gravis. The eyes of all three patients eventually became disabled, and the patients were almost unable to move their eyes in any direction. We termed this condition as "frozen eyes" appearance. We discuss the unique clinical condition and follow the electromyographic and neuro-ophthalmological characteristics. The patients all suffered from ptosis, mild to moderate exotropia, and facial and oropharyngeal weakness. All of the patients responded to the neostigmine test positively at the early stage. Two of them were seropositive. The results of electromyography for two of these three cases were abnormal. The average duration of follow-up was 5 years. The treatments included conventional recession and resection procedures with adjustable sutures for strabismus and frontalis suspension for blepharoptosis. The patients achieved stable satisfactory results in over one-and-a-half years of postoperative follow up. |
本系統中英文摘要資訊取自各篇刊載內容。