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題 名 | Retroperitoneal Schwannoma Clinical Experience in Fifteen Cases=後腹腔神經鞘瘤十五例之臨床經驗 |
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作 者 | 林敏哲; 劉銘; 雷永耀; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 25:6 民81.11-12 |
頁 次 | 頁1456-1460 |
分類號 | 416.242 |
關鍵詞 | 後腹腔神經鞘瘤; |
語 文 | 英文(English) |
中文摘要 | 後腹腔神經鞘瘤(retroperitoneal schwannoma)臨床上極為罕見,臺北榮總自1980年一月至 1991年五月,十二年僅發現十五例,其中良性十四例,惡性一例,占所有後腹腔腫瘤的6.1%,以及所有神經鞘瘤的2.6%。十五例中僅一例惡性後腹腔神經鞘瘤合併有von Recklinghausen氏病。因其複雜而非特異性的臨床表現,手術前正確之診斷十分困難。我們回溯研究這十五例病人,發現囊狀變性(cystic change)是最常見的組織學變化,並為其放射線診斷的特徵之一。90%的超音波顯示為混合型(echocomplex)的圖象。88.9%的電腦斷層為不均勻密度(inhomogenous density)的圖象。所有十四例良性後腹腔神經鞘瘤都接受了外科手術完整切除,預後良好,追踪期自五個月至118個月(平均45.6個月),沒有局部復發的情形。唯一一例惡性後腹腔神經鞘瘤因己侵犯附近器官,手術後僅存活一個月,預後甚差。 |
英文摘要 | Retroperitoneal schwannomae are rare neoplasmas arising from the Schwann cells of the neural sheath. Since January 1980, 15 patients (7 men and 8 women), 22 to 59 years old (mean age 45.8) have been diagnosed in this hospital with retroperitoneal schwannoma, including 14 patients with benign, and 1 patient with a malignant tumor. These represented 6.1% of the patients with retroperitoneal tumors, and 2.6% of the patients with schwannoma encountered at our hospital. Among the 15 patients, only the one with a malignant tumor had a history of von Recklinghausen's disease. Accurate preoperative diagnosis was difficult because of vague, nonspecific clinical presentations. Cystic degeneration was the most common histological findings, and might be considered one of the roentgenographic features of the schwannoma. Echocomplex pattern consisted of 90% of sonographic findings; 88.9% showed inhomogeneous density of CT scan images. All fourteen of the patients with benign retroperitoneal schwannoma received complete excision and the prognosis was good. No local recurrence was found after a follow-up period of 5 to 118 months (mean followup 45.6 months). The single patient with malignant retroperitoneal schwannoma died within a month after exploratory laparotomy. |
本系統中英文摘要資訊取自各篇刊載內容。