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題 名 | Thoracic Spinal Extradural Angiolipoma--A Case Report and Literature Review=胸椎硬脊膜外血管性脂肪瘤--病例報告及文獻回顧 |
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作 者 | 鄭進源; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 24:2 民80.03-04 |
頁 次 | 頁646-650 |
分類號 | 416.292 |
關鍵詞 | 胸椎硬脊膜外血管性脂肪瘤; |
語 文 | 英文(English) |
中文摘要 | 硬脊膜外血管性脂肪瘤是一種少見的良性腫瘤,它包含了血管和脂肪組織。1890年Bernbruch首先發表這種病例。回顧過去文獻的報告共統計出36個病例。此腫瘤的組織學來源包括由原始的多功能問質細胞衍生而來或是一種先天性畸胎瘤(Hamartoma)。本病例是一位65歲女性病患,入院後主訴二年多之下肢麻木,症狀時好時壞,此次係因兩下肢無力及偶發性小便失禁,住院後經過理學檢查懷疑胸椎病灶。經過核磁共振掃描,顯示從第四胸椎到第六胸椎硬銷膜外有壓迫性腫塊,鑑別診斷包括硬脊膜外血腫,轉移性黑色素瘤或是脂肪瘤。病人接受手術切除腫瘤,術後病理組織切片檢查證實病人罹患胸椎硬脊膜外血管性脂肪瘤。對於術前確定位置的腫瘤,早期手術治療以期達到神經病變完全復原。本例經手術治療成功,謹提出臨床報告及文獻回顧。 |
英文摘要 | A rare case of thoracic spinal angiolipoma presenting with extradural spinal cord compression is described. A 65-year-old female developed slowly progressive paraparesis during a two-year period. A plain radiograph of the thoracic spine was normal. Magnetic resonance imaging (MRI) showed an area of high signal intensity in both Tl and T2-weighted images in the posterior extradural space of the thoracic spine from the level of T4 to T6. A bilateral thoracic laminectomy was carried out, and an extradural hypervascular fatty mass, loosely adherent to the dura mater, was disclosed and totally removed. The pathological diagnosis was angiolipoma. The clinical, radiological, and pathological characteristics of spinal extradural angiolipoma are discussed in this paper. These data indicate that the results of early surgical extirpation of this tumor are usually excellent. |
本系統中英文摘要資訊取自各篇刊載內容。