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題 名 | Leiomyosarcome of the Duodenum (Report of Five Cases)=十二指腸惡性平滑肌肉瘤 |
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作 者 | 王嘉修; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 10:4 1977.12[民66.12] |
頁 次 | 頁269-279 |
關鍵詞 | 十二指腸; 惡性平滑肌肉瘤; |
語 文 | 英文(English) |
中文摘要 | 十二指腸惡性平滑肌肉瘤為一種罕見的腫瘤,從1920年首先報告到1976年為止,文獻上,總共只有一百例左右。從民國55年元月到66年3月之間,共有五例在臺大醫院外科接受手術治療。 本病的主要症狀為上消化道出血,上腹痛,及腹部腫塊。臨床檢查方面,上消化道鋇劑攝影或低張性十二指腸攝影可見到粘膜下腫瘤引起的各種變化,選擇性血管攝影可見到更特有的變化以供鑑別診斷,而十二指腸內視鏡檢查加上活體切片檢查,可提供更正確的手術前診斷。急性大量的上消化道出血的情況下手術而查無其他病變時,應考慮到十二指腸惡性平滑肌肉瘤所引致的可能性。 本病的治療為廣泛的手術切除,由於腫瘤一般都很大,所以往往要做胰十二指腸切除術。本報告的五例中,有二側施行胰十二指腸切除術,其他三例則無法切除,其中二例僅作改道手術,另一例則僅做剖腹探查及切片檢查。 十二指腸惡性平滑肌肉瘤在發病過程上是屬於生長較慢及惡性度較低的一種腫瘤,在十二指腸的惡性腫瘤中其預後為最好。 |
英文摘要 | Leiomyosarcoma of the duodenum is a rare malignancy. Up to 1976, there were only about 100 cases reported in the world literature. We have added 5 cases to the above number. Leiomyosarcoma of the duodenum should be included in the differential diagnosis of patients with upper gastrointestinal bleeding, upper abdominal pain and palpable abdominal mass. Barium meal study, hypotonic duodenography, duodenofiberscopy plus biopsy, and selective angiography would be helpful in the preoperative diagnosis. The tumor is a slow growing and low grade malignancy. Metastasis is relatively uncommon. Surgical extirpation, regardless of the size of tumor if no distant metastasis, is the treatment of choice. Prognosis is not optimistic, but not as pessimistic as that of carcinoma and the other malignancies of the duodenum. |
本系統中英文摘要資訊取自各篇刊載內容。