頁籤選單縮合
題 名 | 以快速進行性失智來表現庫賈氏病的老年病人=Creutzfeldt-Jakob Disease Presenting as Rapidly Progressive Dementia in an Elderly Patient |
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作 者 | 吳怡萱; 盧豐華; 張家銘; | 書刊名 | 臺灣老年醫學暨老年學雜誌 |
卷 期 | 12:3 2017.08[民106.08] |
頁 次 | 頁207-215 |
分類號 | 417.7827 |
關鍵詞 | 庫賈氏病; 失智症; 老年人; Creutzfeldt-Jakob disease; Dementia; Elderly; |
語 文 | 中文(Chinese) |
中文摘要 | 庫賈氏病是相當罕見的疾病,發生率約為百萬分之一。它是一種有很長潛伏期的神經退化性疾病,其中以散發型最多,占85%,病患多為中老年人,發病初期的表徵包括快速認知功能受損,導致記憶力減退、人格改變和幻覺。其他常見的症狀包括焦慮、抑鬱、偏執、強迫症狀和精神病等。有時還會伴隨著語言障礙、肌躍症、平衡和共濟失調、步態變化、僵硬姿勢和癲癇發作。然而,對不熟悉庫賈氏病的臨床醫師來說,要診斷老年人具有此病可能充滿挑戰。因此,我們提出一位以失智症病情進展迅速為初期表現的71歲男性病人,最後診斷為散發性庫賈氏病的病例供參考。 |
英文摘要 | A highly rare (occurring in approximately in of every in million people) human prion disease, Creutzfeldt-Jakob disease (CJD) is a neurodegenerative disease with a long incubation period and progressing inexorably once clinical symptoms emerge. Sporadic CJD accounts for nearly 85% of the cases and usually occurs in middle-aged and elderly persons. The initial symptom of CJD is rapidly progressive impairment of cognition, leading to memory loss, personality changes, and hallucinations. Other frequent features include anxiety, depression, paranoia, obsessive-compulsive symptoms, and psychosis, which may be accompanied by physical problems like speech impairment, myoclonus, balance and ataxia, changes in gait, rigid posture, and seizures. However, clinical diagnosis can be a challenge for physicians inexperienced with the disease, especially when it occurs in elder patients. We here present a 71-year-old male with first presentation of rapidly progressive dementia later confirmed as sporadic CJD. |
本系統中英文摘要資訊取自各篇刊載內容。