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題 名 | Dental Treatment of a Child with Kabuki Syndrome--A Case Report=歌舞伎症候群患者的牙科治療--病例報告 |
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作 者 | 陳嘉容; 陳亮如; | 書刊名 | 臺灣兒童牙醫學雜誌 |
卷 期 | 18:1 2018.03[民107.03] |
頁 次 | 頁18-23 |
分類號 | 416.9 |
關鍵詞 | 歌舞伎症候群; 牙; Kabuki syndrome; Dental; |
語 文 | 英文(English) |
中文摘要 | 歌舞伎症候群是一種先天性多重異常的疾病,往往伴隨著智能遲緩,由於病患之臉部特徵類似歌舞伎演員,故以此命名。本病歷報告為一位患有歌舞伎症候群之三歲小女孩於全身麻醉下接受牙科治療,因為此類患者常伴隨有先天性心臟病,且可能有影響插管之構造異常,於麻醉前應審慎評估病史,並會診小兒科醫師及麻醉科醫師。術後更應該加強教導監護者口腔清潔技巧,並安排定期每三個月回診檢查。 |
英文摘要 | Kabuki syndrome(KS) is named because the facial features resemble the makeup of Kabuki actors. This case report presents a 3-year-old girl with Kabuki syndrome who had long palpebral fissures with the eversion at the outside edges of lower eyelids; long eyelashes; jug ears and short fifth fingers. Intraoral examination found delayed eruption of primary second molar, high-vaulted palate and multiple caries. Due to the young age and poor compliance, full mouth dental rehabilitation under general anesthesia was suggested. Because of the possibility of heart abnormalities, consultation with pediatrician and anesthesiologists before full mouth rehabilitation were necessary. Oral hygiene instruction and periodical recall every 3 months have been emphasized and advised to the parents. |
本系統中英文摘要資訊取自各篇刊載內容。