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題 名 | 紫質症的治療與文獻探討=Porphyria Treatment and Literature Review |
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作 者 | 陳昱彣; 張翌君; 黃學揚; 魏春生; 郭力誠; | 書刊名 | 藥學雜誌 |
卷 期 | 31:1=122 2015.03[民104.03] |
頁 次 | 頁91-95 |
分類號 | 415.62 |
關鍵詞 | 紫質症; 血基質; Porphyria; Heme; |
語 文 | 中文(Chinese) |
中文摘要 | 紫質症 (porphyria) 是先天酵素血基質代謝異常的遺傳顯性疾病或後天經由誘發因 子促成病狀所產生的罕見疾病。有些人有遺傳基因的存在,但也有未發病情形;另外 有些人卻因為外來刺激因子的因素而誘發症狀的產生,經幾次就診看不同科別的醫師 而能被確診為紫質症的人數並不多,但患者卻早已經歷病痛的折磨,且因醫療團隊無 法有效解決問題,導致病人不願再次求醫就診而放棄治療,更影響其日常的生活。 紫質症的種類有八種,其臨床症狀包含:不明原因腹痛、低血鈉、尿液照光變色 等。本文將各類別紫質症的臨床症狀,藉由文獻回顧分析來提供醫療人員對於其疾病 的診斷治療方針及預防,將有利於患者接受正確治療,進而提昇其生活品質。 |
英文摘要 | Porphyria is an autosomal dominant or induce clinical symptoms to be a rare disease cause by enzyme disorders with heme biosynthesis or stimulate facts trigger. Some patients have genetic gene without clinical presentation. However, other part of them present with symptoms because of stimulating factors trigger. After transfer to many different types of clinical physician under diagnosis, these patients may give up their treatment and had bad quality of life because of unable diagnosis and suffers from porphyria. This article will discuss eight different types of porphyria, their clinical symptoms include: unreasonable abdomen pain, hyponatremia, propurine et al. The treatment and literature review to be able provide medical health team acknowledge and help their patient and get right treatment. Also, notice stimulating factors may disable their symptoms trigger and benefit for patients to receive proper treatment and have a better life. |
本系統中英文摘要資訊取自各篇刊載內容。