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題 名 | Anti-synthetase Syndrome Presenting as an Interstitial Lung Disease: A Case Report=抗合成酶症候群以間質性肺病來表現:個案報告 |
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作 者 | 葉宏明; 陳長宏; 李文宏; | 書刊名 | 胸腔醫學 |
卷 期 | 29:5 2014.10[民103.10] |
頁 次 | 頁281-286 |
分類號 | 415.46 |
關鍵詞 | 多發性肌炎; 間質性肺病; 抗合成酶症候群; 抗Jo-1抗體; Polymyositis; Interstitial lung disease; Anti-synthetase syndrome; Anti-Jo-1 antibodies; |
語 文 | 英文(English) |
中文摘要 | 抗合成酶症候群是發炎性肌炎的一種亞型,特點在於發炎性肌炎或皮肌炎合併對稱性關節炎、間質性肺病、技工手、發燒、光過敏和血中測得抗合成酶,通常會因為肺部病變不可逆性進展而預後不佳。我們在此報告一位64歲男性,以兩手關節炎,胸部X光出現間質性肺病和抗Jo-1抗體來表現。早期診斷可以提早施用免疫抑制劑而得到較佳之預後。 |
英文摘要 | Anti-synthetase syndrome is a serological subtype of idiopathic inflammatory myositis characterized by the production of antisynthetase antibodies and the development of dermatomyositis or polymyositis, symmetrical arthritis, interstitial lung disease, mechanic's hand, fever, and photosensitivity. It has a generally poor prognosis, mainly due to irreversibly progressive pulmonary involvement. We report the case of a 64-year-old man who presented with symmetrical upper extremity arthralgia, interstitial lung infiltrates in chest films and anti-Jo-1 antibody. Early diagnosis followed by immunosuppressive therapy is essential to prevent the development of respiratory failure in these patients. |
本系統中英文摘要資訊取自各篇刊載內容。