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題 名 | Sinonasal Diffuse Large B Cell Lymphoma=鼻及鼻竇B細胞淋巴瘤 |
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作 者 | 李泳姿; 洪瑞隆; | 書刊名 | 臺灣癌症醫學雜誌 |
卷 期 | 28:4 2012.12[民101.12] |
頁 次 | 頁183-188 |
分類號 | 416.871 |
關鍵詞 | 鼻及鼻竇淋巴瘤; 瀰漫性大B細胞淋巴瘤; Sinonasal lymphoma; Diffuse large B cell lymphoma; |
語 文 | 英文(English) |
中文摘要 | 從鼻腔及鼻竇長出之非何杰氏淋巴瘤是非常罕見的,我們報告一位 71 歲的男性病 患,開始以左側鼻腔腫瘤表現,並有鼻塞、流鼻血及嗅覺喪失等症狀。內視鏡鼻竇手術 及切片病理報告顯示瀰漫性大 B 細胞淋巴瘤。此病人在接受了四次 CHOP 化學治療及鞏 固性的放射治療後,有 6 年的完全緩解狀態。其後淋巴瘤於右側鼻腔復發,同時於周邊 血液可見芽細胞,其後證實為淋巴瘤併骨髓侵犯所導致,腦脊髓液也發現有淋巴細胞侵 犯。雖然給予挽救性的化學治療,此病患於疾病復發後三個月左右死亡。鼻及鼻竇 B 細 胞淋巴瘤的臨床表現具獨特性,但目前為止尚未有一致的治療建議。 |
英文摘要 | Non-Hodgkin lymphoma arising from the sinonasal tract is rare. We present hereby a 71 year-old man with the chief complaints of a left nasal mass, nasal obstruction, bleeding and anosmia. Functional endoscopic sinus surgery and biopsy yielded diffuse large B cell lymphoma. The patient remained disease-free for about 6 years after 4 courses of CHOP (Cyclophosphamide, doxorubicin, vincristine, prednisolone) and consolidative involved field radiotherapy, and then the lymphoma recurred in the right nasal cavity. Lymphoblasts were present in the peripheral blood, which turned out to have originated from lymphoma with bone marrow involvement. A cerebrospinal fluid study was also positive for lymphoblasts. The patient died 3 months after the disease recurrence despite salvage chemotherapy. The clinical characteristic of sinonasal diffuse large B cell lymphoma is distinct, and there is no consensus regarding standard treatment in this rare group of patients. |
本系統中英文摘要資訊取自各篇刊載內容。