頁籤選單縮合
題 名 | Trichogerminoma: A Case Report, Historical Review and Reconceptualization=毛囊生殖胚瘤(Trichogerminoma):病歷報告、歷史回顧與概念重構 |
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作 者 | 黃致翰; 陳信翰; 林智一; 張家寧; | 書刊名 | 臺灣整形外科醫學會雜誌 |
卷 期 | 21:3 2012.09[民101.09] |
頁 次 | 頁230-235 |
分類號 | 415.78 |
關鍵詞 | 毛囊生殖胚瘤; Trichogerminoma; Trichoblastoma; Hair follicle neoplasms; Hair germ tumors; |
語 文 | 英文(English) |
中文摘要 | 背景:毛囊生殖胚瘤是一種罕見的良性毛囊腫瘤,其分化型態朝向毛囊生殖胚。自從1992年Sau等人首次提出毛囊生殖胚瘤的概念並且提出十四個個案系列以後,至今只有三個個案報告。目的及目標:我們報告一位蒙古種男性的下陰部的毛囊生殖胚瘤的個案,而生長在此種族或此區域的個案尚未被報告過。我們也會回顧相關的文獻。材料及方法:一位56歲的蒙古種男性在他的下陰部有一個一公分大小的結節存在好幾年了。我們進行了切除性的切片,並且根據組織學型態,診斷此病灶為毛囊生殖胚瘤。結果:術後的恢復相當平順。追蹤三年並無復發。結論:毛囊生殖胚瘤是一種罕見的良性皮膚附件腫瘤,並且應當屬於所有毛囊生殖腫瘤(hair germ tumors)的範疇中。完整的腫瘤切除是治療的第一選擇。典型的顯微病理發現為確定的診斷方式。毛囊生殖胚瘤的疾病實體是毫無疑問存在的,因為其具有可識別的型態分化,且此型態分化有別於毛囊生殖母細胞瘤。我們並不能只因為毛囊生殖胚瘤很罕見,就認為它只是一個虛構出來的概念。 |
英文摘要 | Background: Trichogerminoma is a rare benign follicular tumor with differentiation toward the hair germ. Since the first introduction of 14 cases of trichogerminoma by Sau et al in 1992^1, there were only three cases have been reported until now^2-3. Aim and objectives: We presented one case of trichogerminoma on the lower pubic area of a Mongolian man, which had not been reported of such location or race, and a review of the relevant literatures will also be highlighted. Materials and Methods: A 65-year-old Mongolian man had one nodule of 1cm in size on his lower pubic area for several years. We performed excisional biopsy and histologically diagnosed the lesion with trichogerminoma. Results:Post-operative course was smooth. There was no recurrence after three years follow-up. Conclusion: Trichogerminoma is a rare benign skin adnexal tumor within the spectrum of hair germ tumors. Complete excision of the tumor is a prior choice of treatment. Classical pathological findings are the definitely diagnosis. The entity of trichogerminoma exists without doubt by the identifiable morphodifferentiation in comparison with trichoblastoma. We can not treat trichogerminoma as a fabricated concept just because its rareness. |
本系統中英文摘要資訊取自各篇刊載內容。