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題 名 | Leiomyosarcoma of the Mediastinum: An Extremely Rare Case=縱膈腔平滑肌惡性肉瘤:極罕見之病例 |
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作 者 | 李彥龍; 李憲斌; 李瑞英; 姜宏興; 陳莉君; 周世華; | 書刊名 | 胸腔醫學 |
卷 期 | 27:5 2012.10[民101.10] |
頁 次 | 頁299-304 |
分類號 | 416.226 |
關鍵詞 | 縱膈腔; 鎖骨上; 平滑肌惡性肉瘤; Mediastinum; Supraclavicle; Leiomyosarcoma; |
語 文 | 英文(English) |
中文摘要 | 惡性平滑肌腫瘤大部分發生在子宮及消化道因其含有大量的平滑肌。在縱膈腔的軟組織中,這些腫瘤是相當罕見的。在此,我們報導了一個44歲男性,本身患有第一型神經纖維瘤,因呼吸喘、胸痛及左鎖骨上硬塊就診。經檢查後,診斷出延伸於縱膈腔及鎖骨上的平滑肌惡性肉瘤。因呼吸窘迫及左上肢功能受損,病人接受減瘤手術,術後病人拒絕化學治療及放射線治療。不幸地,三個月後腫瘤復發,七個月後病人死亡。 |
英文摘要 | Malignant smooth muscle tumors usually develop in the uterus and gastrointestinal tract due to the abundance of smooth muscle. They rarely develop in the soft tissue of the mediastinum. We report a 44-year-old male with neurofibromatosis type I who suffered from leiomyosarcoma extending between the left supraclavicle and the left-side middle mediastinum. The patient received debulking surgery to salvage the compromised airway and disabled upper limb. He then refused adjuvant therapy and expired 7 months postoperatively due to recurrence. To our knowledge, this type of case has never been reported in the literature. |
本系統中英文摘要資訊取自各篇刊載內容。