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題 名 | Hepatic Angiomyolipoma--A Rare Presentation with Recurrence and Intrahepatic Metastases=肝臟血管肌肉脂肪瘤--一個少見的復發性的肝內轉移案例 |
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作 者 | 何恭誠; 劉建良; 李居仁; 劉滄柏; 柯文清; 林俊昌; | 書刊名 | 臺灣癌症醫學雜誌 |
卷 期 | 27:2 2011.04[民100.04] |
頁 次 | 頁71-77 |
分類號 | 416.246 |
關鍵詞 | 肝腫瘤; 血管肌肉脂肪瘤; Liver tumor; Angiomyolipoma; |
語 文 | 英文(English) |
中文摘要 | 血管肌肉脂肪瘤被認為是的良性的腫瘤,主要含有脂肪、血管及肌肉三大組織型態,常發生在腎臟,並與結節性硬化症有關。肝臟血管肌肉脂肪瘤(hepatic angiomyolipoma, HAML)是一種罕見的肝腫瘤。雖然肝臟血管肌肉脂肪瘤表現良性的病理特性,但是仍可能出現惡性行為,例如復發。本文將報告一個曾經接受過肝臟血管肌肉脂肪瘤切除的病例,四年後復發再次接受外科切除。 |
英文摘要 | Angiomyolipoma is a histologically benign tumor composed of adipose tissue, smooth muscle and blood vessels. It is usually seen in the kidney associated with tuberous sclerosis. Hepatic angiomyolipoma (HAML) is thought to be a rare benign liver tumor. Although HAML has benign pathologic features, it is still possible for it to manifest malignant behavior, such as recurrence. We report on a 38-year-old patient with HAML recurrence 4 years after surgical resection of the initial tumor. |
本系統中英文摘要資訊取自各篇刊載內容。