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頁籤選單縮合
題 名 | 戈罕氏症=Gorham-stout Disease |
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作 者 | 李沛璋; 吳玉琮; 蘇剛正; 李毓芹; | 書刊名 | 臨床醫學 |
卷 期 | 68:3=405 2011.09[民100.09] |
頁 次 | 頁236-242 |
分類號 | 416.26 |
關鍵詞 | 戈罕氏症; 乳糜胸; 蝕骨; 血管增生; 干擾素; Gorham-stout disease; Chylothorax; Osteolysis; Hemangiogenesis; Interferon; |
語 文 | 中文(Chinese) |
中文摘要 | 戈罕氏症(Gorham-Stout disease)是一種罕見的蝕骨性疾病,主要原因為骨內小血管或淋巴管過度增生而導致的骨質破壞;然而,確切的致病機轉目前仍屬不明。臨床上約有五分之一的病人會合併乳糜胸(chylothorax),這類病人的預後明顯較差。治療方面,可以選擇外科手術、放射線治療、口服抗蝕骨藥物或皮下注射甲型干擾素(Interferon-α)。我們在此藉由一位32歲男性病例,一窺此病的特殊表現,以及病人在使用干擾素後臨床上明顯的改善。 |
本系統中英文摘要資訊取自各篇刊載內容。