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題 名 | 侵犯至鼓室乳突腔之頸靜脈孔腦膜瘤=Jugular Foramen Meningioma with Extension to the Tympanomastoid Cavity |
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作 者 | 王振鴻; 林凱南; | 書刊名 | 臺灣耳鼻喉頭頸外科雜誌 |
卷 期 | 45:1 2010.01-02[民99.01-02] |
頁 次 | 頁20-24 |
分類號 | 415.938 |
關鍵詞 | 頸靜脈孔; 腦膜瘤; Jugular foramen; Meningioma; |
語 文 | 中文(Chinese) |
中文摘要 | 發生在頸靜脈孔之腦膜瘤是非常罕見的。頸靜脈副神經節瘤和神經鞘膜瘤是發生在頸靜脈孔的兩種常見腫瘤。發生在頸靜脈孔之腦膜瘤乃是常見的腦膜瘤在不尋常的位置發生,可分為原發性和次發性。前者是指原發在頸靜脈孔之腦膜瘤,後者是指由顱內腦膜瘤延伸到頸靜脈孔。原發性之頸靜脈孔腦膜瘤臆測是源自頸靜脈孔中頸靜脈竇相關的蜘蛛膜絨毛。本文報告1名44歲女性,主訴是左側長達1年多的漸進性聽力喪失,伴隨著搏動性耳鳴及耳痛。局部檢查可見左側耳膜輕微的突起,聽力檢查顯示左側混合型聽力喪失。顳骨高解析度電腦斷層掃描可見有軟組織在中耳腔。在懷疑中耳腫瘤的診斷下,安排接受鼓室探查手術及乳突鑿開手術,術中看到根基於下鼓室的乳突狀腫瘤佔滿中耳腔。病理檢查證實為腦膜瘤。術後安排核磁造影,看到有一個源自頸靜脈孔之腫瘤,往中耳腔和小腦橋腦角延伸。後續轉介病人到神經外科接受進一步治療,因為腫瘤包覆著腦神經,為避免手術後造成不可逆的併發症,於是安排不完全切除手術,保留靠近腦神經的部份腫瘤。耳部手術後第六年因為持續性耳漏至門診就診,局部檢查發現一鼓出的腫瘤塞滿整個左側外耳道,疑為再發,安排乳突鑿開手術清除腫瘤。根據英文文獻記載,原發性之頸靜脈孔腦膜瘤病例總數不超過一百例,誠屬罕見病例,特此提出報告。 |
英文摘要 | The occurrence of a meningioma within the jugular foramen is extremely rare. It is presumed that primary jugular foramen meningiomas arise from arachnoid-lining cells situated within the jugular foramen. We present the case of a 44-year-old woman who presented with one-year history of left progressive hearing loss and pulsatile tinnitus. Otoscopy revealed mild bulging of left eardrum. Pure tone audiometry revealed mixedtype hearing loss. High resolution computed tomography showed a soft tissue in the middle ear. Under the suspicion of middle ear tumor, she underwent tympanoplasty and radical mastoidectomy. Histopathologic diagnosis was meningioma. Magnetic resonance imaging revealed a enhancing tumor in the jugular foramen with extension to posterior fossa and carotid space. Then she was referred to neurosurgical department for further treatment. Subtotal resection of the jugular foramen meningioma was performed. Six years later, she was suffered from persistent left-sided otorrhea. A papillomatous tumor was noted in the external ear. Palliative mastoidectomy was performed under the suspicision of recurrence of jugular foramen meningioma. |
本系統中英文摘要資訊取自各篇刊載內容。