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題 名 | Inconsistent Immunostaining and Racial Difference in Extramammary Paget's Disease=乳房外柏哲德氏病之免疫染色與人種差異性研究 |
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作 者 | 蔣富強; 朱思穎; 張雲亭; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 27:3 2009.09[民98.09] |
頁 次 | 頁161-169 |
分類號 | 416.69 |
關鍵詞 | 乳房; 柏哲德氏病; 皮膚癌; Extramammary Paget's disease; Cytokeratin 7; Cytokeratin 20; Gross cystic disease fluid protein-15; |
語 文 | 英文(English) |
英文摘要 | Background: Extramammary Paget’s disease (EMPD), an uncommon neoplastic disorder, usually presents as an eczematous patch on the apocrine-rich area. It can be further classifi ed into primary and secondary EMPD by its association with underlying malignancies. The histopathology shows a characteristic intraepidermal atypical clear cell infi ltrate. Objective: To determine whether the histopathologic or immunohistochemical features of EMPD could be used to predict clinical behavior or association with underlying malignancies. Methods: Twenty-two freshly-diagnosed EMPD cases were collected retrospectively in the past 10 years. All were Chinese and their medical records were reviewed. Histopathology of skin specimens were examined and immunohistochemical staining of cytokeratin 7 (CK7), cytokeratin 20 (CK20), and gross cystic disease fl uid protein-15 (GCDFP-15) were performed. Results: None of the cases were proven to be secondary EMPD. The Paget’s cells from all cases were immunopositive for CK7. In 58% of primary EMPD cases, the Paget’s cells had the immunophenotype CK20(-)/GCDFP-15(+). Conclusion: In Chinese patients with EMPD, routine invasive surveys for associated malignancies might be unnecessary. CK7 is a suitable marker for the diagnosis of EMPD due to its high sensitivity. It is unreliable to distinguish between primary and secondary EMPD from their reactivity of CK20 and GCDFP-15. |
本系統中英文摘要資訊取自各篇刊載內容。