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題 名 | Expandable Congenital Lung Cysts: A Case Report=可擴張之先天性肺囊腫:一病例報告 |
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作 者 | 李淑婷; 林隆煌; 陳五常; 那明珠; | 書刊名 | 輔仁醫學期刊 |
卷 期 | 4:2 民95.06 |
頁 次 | 頁107-112 |
分類號 | 415.46 |
關鍵詞 | 先天囊腫性腺瘤樣畸形; 先天囊腫性肺部疾病; 先天性肺囊腫; Congenital cystic adenomatoid malformation; Congenital cystic lung disease; Congenital lung cyst; |
語 文 | 英文(English) |
中文摘要 | 先天囊腫性肺部疾病為一系列相關的先天性異常,其中包括先天性肺氣腫,支氣管囊腫,先天囊腫性腺瘤樣畸形及游離肺。其中先天囊腫性腺瘤樣畸形目前被認為是肺間質在妊娠5到7週時無法成功的誘發部分胎兒支氣管肺泡的分化所致。我們報告一例男性新生兒在出生後出現呼吸困難,壓力性氣胸,及愈來愈大的肺部囊腫,其臨床診斷為先天囊腫性腺瘤樣畸形。在本文中我們敘述此病例的臨床及影像學上的表現,以及首次在此疾病中敘述可擴大的肺部囊腫。 |
英文摘要 | Congenital cystic lung diseases comprise a spectrum of interrelated abnormalities that include congenital lobar emphysema (CLE), bronchogenic cysts, congenital cystic adenomatoid malformation (CCAM), and pulmonary sequestration. CCAM is thought to result from a failure of the pulmonary mesenchyme to induce normal bronchoalveolar differentiation in a part of the fetal lung between the fifth and seventh weeks of gestation. We describe a male newborn who presented with respiratory distress, tension pneumothorax, and expanding lung cysts after delivery; he was clinically diagnosed as having CCAM. We are the first to describe the clinical and image presentations of expandable lung cysts under ventilation. |
本系統中英文摘要資訊取自各篇刊載內容。