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題 名 | Congenital Self-Healing Reticulohistiocytosis Presenting as Hypopigmented Macules and Papules in a Neonate=以白色斑疹及丘疹為表現的先天性自癒性網狀組織細胞增生症 |
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作 者 | 張學倫; 施一新; 郭承統; 賴義傑; 紀景琪; 楊志勛; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 26:2 2008.06[民97.06] |
頁 次 | 頁80-84 |
分類號 | 415.7 |
關鍵詞 | 先天性自癒性網狀組織細胞增生症; 蘭格罕氏組織細胞增生症; Langerhans cell histiocytosis; Congenital self-healing reticulohistiocytosis; Hashimoto-Pritzker disease; Hypopigmentation; |
語 文 | 英文(English) |
中文摘要 | 先天性自癒性網狀組織細胞增生症是蘭格罕氏組織細胞增生症中罕見的一種型態。其特徵是在剛出生或出生數週內在皮膚產生多個或單一紅棕色丘疹、腫塊或水疱而不侵犯其他器官或系統,且會自行痊癒。我們報告一位女嬰以白色斑疹及丘疹呈現於軀幹為表徵。藉由病理檢查及免疫組織學檢查證實為蘭格罕氏組織細胞增生症。我們提醒皮膚科醫師注意先天性自癒性網狀組織細胞增生症之罕見表現方式;當嬰兒身上呈現白色病灶時,應將本病列入鑑別診斷。 |
英文摘要 | Congenital self-healing reticulohistiocytosis, also known as Hashimoto-Pritzker disease) is a rare variant of Langerhans cell histiocytosis. It is characterized by developing multiple or single red-brown papules, nodules or vesicles at birth or first few weeks of life and involutes spontaneously without systemic involvement of other organs. We report a rare case of female neonate presented with multiple white macules and papules on trunk. Langerhans cell histiocytosis is diagnosed by histological examination and immunohistochemical study. We remind dermatologists to be aware of this rare presentation and should put it into differential diagnosis lists when facing hypopigmented lesions in a neonate. |
本系統中英文摘要資訊取自各篇刊載內容。