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題 名 | Frontal Fibrosing Alopecia--A Case Report=前額纖維化禿髮--病例報告 |
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作 者 | 高嘉懋; 蕭正祥; 蘇琳惠; 徐毓聆; 蔡宗樺; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 26:1 2008.03[民97.03] |
頁 次 | 頁34-38 |
分類號 | 415.7752 |
關鍵詞 | 前額纖維化禿髮; Frontal fibrosing alopecia; Lichen planopilaris; Primary cicatricial alopecia; |
語 文 | 英文(English) |
中文摘要 | 一位52歲女性在其前額、顳額、和頂額有漸進性的髮線後退(1至3.5公分不等)。這些區域同時有表面光亮、輕度搔癢、不完全落髮、以及些微的毛囊開口消失的情形。尚未落髮的毛孔周圍則主要有過度角化伴隨局部些微變紅的變化。兩側眉毛也幾乎掉光,但身體其他部分的毛髮則是正常。寶驗室檢查包括有一般生化試驗、甲狀腺功能、抗核抗體、C型肝炎標記、以及性激素全部都無異常發現。組織學可見在毛囊周圍,特別是上半部,有少量的淋巴球波浸潤及明顯的纖維化,而真皮乳突層內並沒有大量苔癬樣發炎的現象。直接免疫螢光染色班沒有發現IgG, IgA, C3其中任何一者在毛囊基底膜的沈積。根據特異的臨床表現以及組織學上支持的特徵,我們報告了一個典型的前額纖維化禿髮的病例。再者,由於至今仍無有效的療法,及早診斷此疾病,且與病人溝通後使其瞭解疾病的預後是非常重要的。 |
英文摘要 | A 52 year-old female presented with a 2-year history of progressive hairline recession over frontotempro-parietal area (1 to 3.5cm variably). Shiny affected area, mild pruritus, incomplete hair loss, and subtle loss of follicular openings were also noted. Follicular hyperkeratosis and focal minimal perifollicular erythema were found at the hairline. Nearly total absence of eyebrow hairs was observed, but all other parts of body hair appeared normal. Laboratory tests. including routine biochemistry tests, thyroid function, antinuclear antibodies, and hepatitis C test, showed no abnormalities. Sex hormones were also within normal range. Histologically, there were scanty lymphocytic infiltrate and marked fibrosis around hair follicles, especially the isthmus and infundibulum portion, without lichenoid inflammation its she papillary dermis. The direct immunofluorescence test did not show the deposition of immunoreactants in the follicular basement membrane zone. It is consistent with a case of frontal fibrosing alopecia (FFA) with characteristic clinical presentation and supporting histologic features. Furthermore, owing to the limited effectiveness of treatment, early diagnosis and communication with patients about the prognosis of FFA is important. |
本系統中英文摘要資訊取自各篇刊載內容。