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題 名 | Proximal-Type Epithelioid Sarcoma--A Case Report and Review of the Literature=近端上皮樣肉瘤--病例報告及文獻回顧 |
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作 者 | 黃鴻怡; 王伯涵; 邱琬婷; 吳毅穎; 胡淑玲; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 25:4 2007.12[民96.12] |
頁 次 | 頁274-278 |
分類號 | 415.692 |
關鍵詞 | 近端上皮樣肉瘤; 惡性腫瘤; Epithelioid sarcoma; Rhabdoid feature; |
語 文 | 英文(English) |
中文摘要 | 近端上皮樣肉瘤是一種少見的軟組織惡性腫瘤,主要發生於年輕至中年人的身體近端處。組織學上是以大的多角形細胞,伴隨空泡狀細胞核及顯著的核仁和常見的類橫紋形態。我們在此報告一位27歲女性於會陰部罹患近端上皮樣肉瘤,病患於切片診斷後即接受腫瘤廣泛性切除、左側腹股溝淋巴結切除及裂層皮膚移植。病理報告顯示在真皮及皮下有一界限不明之腫瘤,此腫瘤主要是由大型卵圓狀類上皮細胞所構成,淋巴結並沒有發現腫瘤細胞的存在。此外我們也回顧文獻上關於近端上皮樣肉瘤的臨床、病理、及免疫組織特性。重要的是近端上皮樣肉瘤比起傳統末端上皮樣肉瘤臨床的預後更差。 |
英文摘要 | Proximal-type epithelioid sarcoma is a rare, malignant soft-tissue tumor occurring in the proximal body sites of young to middle-aged adults and microscopically shows sheets of large polygonal cells with vesicular nuclei, prominent nucleoli and frequent rhabdoid features. Herein, we report a 27-year-old woman with proximal-type epithelioid sarcoma over the pubic area. The patient underwent wide excision, left inguinal lymph node dissection and split-thickness skin graft after biopsy proof. Pathological results showed an ill-defined nodule composed of large oval epithelioid cells in the dermis and subcutis. The dissected lymph nodes were free of tumor cells. We also review the literature regarding the clinical, pathologic and immunohistochemical features of proximal-type epithelioid sarcoma. Importantly, proximal-type epithelioid sarcoma has a much worse prognosis than the classical, distally located ones. |
本系統中英文摘要資訊取自各篇刊載內容。