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題 名 | Abdominal Aortic Dissection with Acute Mesenteric Ischemia in a Patient with Marfan Syndrome=Marfan氏症候群:以腹主動脈剝離合併急性腸系膜動脈缺血來表現 |
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作 者 | 賴啟賢; 余承儒; 田雨生; | 書刊名 | 中華醫學會雜誌 |
卷 期 | 69:7 民95.07 |
頁 次 | 頁326-329+CA63 |
分類號 | 416.263 |
關鍵詞 | 腹主動脈剝離; Marfan氏症候群; 腸系膜動脈缺血; Abdominal aortic dissection; Marfan syndrome; Mesenteric ischemia; |
語 文 | 英文(English) |
英文摘要 | Marfan syndrome is an autosomal dominant inherited disorder of connective tissue, with various complications manifested primarily in the cardiovascular system. It potentially leads to aortic dissection and rupture, these being the major causes of death. We report a patient who complained of acute abdominal pain, which presented as acute mesenteric ischemia combined with abdominal aortic dissection. Echocardiography showed enlargement of the aortic root and mitral valve prolapse. Abdominal computed tomography scan revealed acute mesenteric ischemia due to abdominal aortic dissection. Finally, the patient underwent surgery of aortic root replacement and had a successful outcome. Therefore, we suggest that for optimal risk assessment and monitoring of patients with Marfan syndrome, both aortic stiffness and the diameter of the superior mesenteric vein compared with that of the superior mesenteric artery are useful screening methods to detect acute mesenteric ischemia secondary to abdominal aortic dissection. Early diagnosis and early treatment can decrease the high mortality rate of patients with Marfan syndrome. |
本系統中英文摘要資訊取自各篇刊載內容。