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題 名 | Esophageal Atresia with Tracheoesophageal Fistula: Ten Years of Experience in an Institute=食道閉鎖合併氣管食道瘻管:一醫學中心之十年經驗 |
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作 者 | 楊佳鳳; 宋文舉; 鄭玫枝; 陳淑貞; 李昱聲; 曹珮真; 黃碧桃; 魏拙夫; 錢大維; 劉君恕; | 書刊名 | 中華醫學會雜誌 |
卷 期 | 69:7 民95.07 |
頁 次 | 頁317-321+CA61 |
分類號 | 416.216 |
關鍵詞 | 先天性異常; 食道閉鎖; 氣管內支架; 氣管食道瘻管; Congenital anomalies; Esophageal atresia; Intratracheal stent; Tracheoesophageal fistula; |
語 文 | 英文(English) |
英文摘要 | Background: Esophageal atresia (EA), tracheoesophageal fistula (TEF), or both is a complicated problem. The purpose of this study was to evaluate the outcomes and postoperative complications in patients with EA/TEF who were admitted to our hospital. Methods: In total, 15 patients were enrolled from 1994 to 2003, including 8 males and 7 females. Patient demographics, associated anomalies, and outcomes were analyzed. Results: The most common variant was EA with a distal TEF (type C), which occurred in 12 patients (80%). The latter had associated congenital anomalies, and cardiac anomalies were the most frequent, occurring in 8 patients (53.3%). Of the 6 cases who had life-threatening anomalies, 4 (66.7%) died, and of the 9 cases who had no life-threatening anomalies, 2 (22.2%) died. Tracheomalacia and/or stenosis were diagnosed in 8 patients (66.7%) postoperatively. Though 3 of the 4 cases who suffered from dying spell received intratracheal stent implantation, 2 cases still died. Conclusion: The survival rate of the patients with EA/TEF is influenced mainly by associated life-threatening anomalies. TMS combined with a history of dying spell may be the major fatal complication. |
本系統中英文摘要資訊取自各篇刊載內容。