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題 名 | Primary Hepatic Malignant Fibrous Histiocytoma with Chest Wall Invasion: Report of a Case=以胸壁腫瘤為唯一臨床表現的原發性肝臟惡性纖維組織細胞瘤:病例報告 |
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作 者 | 顏至謙; 趙宏明; 張保欽; 劉光益; 奚聖川; | 書刊名 | 臺灣外科醫學會雜誌 |
卷 期 | 41:2 2008.03-04[民97.03-04] |
頁 次 | 頁67-70 |
分類號 | 416.246 |
關鍵詞 | 肝臟; 惡性纖維組織細胞瘤; Liver tumor; Chest wall tumor; Malignant fibrous histiocytoma; |
語 文 | 英文(English) |
中文摘要 | 惡性纖維細胞瘤是成年人晚期最常見的軟組織肉瘤。此細胞瘤傾向於發生在四肢的深部軟組織,而極少發生在肝臟。我們提出一個以胸壁腫瘤爲唯一表現的病例報告。此病人在此次住院前兩個月開始感到右後外側的胸壁有疼痛及腫脹。住院後接受身體理學檢查、血液常規檢查、胸腹部的超音波及電腦斷層檢查。檢查報告指出在肝臟的後葉有一個低密度分界不明顯的腫瘤並且直接侵犯到右後外側胸壁。來自胸壁腫瘤的細胞切片病理報告爲惡性纖維細胞瘤。腫瘤細胞的組織化學免疫染色在CD-68和vimentin呈現陽性反應而在甲胎兒蛋白和癌胚抗原呈現陰性反應。此病人在確定診斷兩個月後死亡。肝臟的惡性纖維細胞瘤雖然極爲少見但還是須放在肝臟腫瘤的鑑別診斷中。由於其惡性度,本病應早期診斷,並以根治性外科手術完全切除腫瘤。 |
英文摘要 | Malignant fibrous histiocytoma is the most common soft tissue sarcoma of late adult life. This tumor tends to occur in the deep soft tissue of the extremities, but rarely develops in the liver. We report a patient who presented with chest wall tumor as the only initial symptom. He complained of right back pain with swelling in the right postero-lateral chest wall, which he had first noticed one month before. Physical examination and routine blood studies were performed, as well as abdominal ultrasound and computerized tomography of the thorax and abdomen. A poorly circumscribed hypodense mass lesion was found in the posterior segment of the liver, with direct invasion of the chest wall. Tissue biopsy of the chest wall tumor led to the diagnosis of malignant fibrous histiocytoma. The immunohistochemical study showed that the tumor cells were positive for CD-68 and vimentin stains, and negative for alpha-fetoprotein, TTF1, HMB45 and carcinoembryonic antigen (CEA). The patient died two months after initial diagnosis. We suggest that primary hepatic malignant fibroid histiocytoma, though rare, should be considered in the differential diagnosis of liver tumor. Early and complete surgical removal of primary hepatic malignant fibroid histiocytoma is necessary because of the aggressive nature of the tumor. |
本系統中英文摘要資訊取自各篇刊載內容。