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題 名 | Repeated Aggressive Surgical Debulking Results in Long-Term Survival in a Patient with Urachal Adenocarcinoma and Pseudomyxoma Peritonei=臍尿管癌造成罕見之腹腔假黏液瘤--經反覆積極性減積手術治療後長期存活之病例報告 |
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作 者 | 吳柏鋼; 李明哲; 陳華宗; 周紹賓; 許永祥; | 書刊名 | 慈濟醫學 |
卷 期 | 19:1 2007.03[民96.03] |
頁 次 | 頁32-35 |
分類號 | 416.274 |
關鍵詞 | 臍尿管癌; 腹腔假黏液瘤; 減積手術; Pseudomyxoma peritonei; Urachal adenocarcinoma; Debulking surgery; |
語 文 | 英文(English) |
英文摘要 | Pseudomyxoma peritonei (PMP) is an unusual condition characterized by massive mucinous ascites associated with peritoneal and omental implantation of tumors. Most cases of PMP arise from the appendix or ovary, but rarely from urachal adenocarcinoma. Although urachal adenocarcinoma with PMP is very difficult to cure and has a poor prognosis, long-term suvival can still be achieved with repeated surgical debulking. We report an unusual case of PMP caused by mucinous adenocarcinoma arising from urachus in a 39 year-old man. Direct tumor invasion to the urinary bladder wall, metastasis to the spleen and peritoneal seeding of tumor were found. Surgical debulking combined with intraperitoneal chemotherapy was performed during the first laparotomy in 1997. During follow up, recurrent disease was diagnosed and five additional aggressive debulking sugeries were performed. The patient has survived for more than mine years and is doing well. |
本系統中英文摘要資訊取自各篇刊載內容。