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頁籤選單縮合
題 名 | Rhabdomyosarcoma of the Kidney Mimicking Urothelial Cancer=腎臟橫紋肌肉瘤以類似尿路上皮癌的型式來呈現 |
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作 者 | 唐守宏; 高鴻偉; 曹智惟; 黃奕烝; 孫光煥; 查岱龍; 李祥生; | 書刊名 | 臺灣泌尿科醫學會雜誌 |
卷 期 | 17:4 民95.12 |
頁 次 | 頁153-156 |
分類號 | 416.273 |
關鍵詞 | 橫紋肌肉瘤; 腎臟; 腫瘤; Rhabdomyosarcoma; Kidney; Neoplasm; |
語 文 | 英文(English) |
中文摘要 | 腎臟的惡性腫瘤中,肉瘤是相對少見的種類,而腎臟肉瘤中的的橫紋肌肉瘤則更為罕見,這類疾病幾乎都以腎實質腫塊的型式來表現,且預後極差,幾乎都於診斷確認兩年內死亡。在本病例報告中,患者為七十七歲女性,她因血尿求診,影像檢查結果發現右側腎盂有一大小為2×2×1.8公分的腫塊,臨床上因此初步懷疑為此為尿路上皮癌症。患者因此接受了右腎切除加膀胱袖口切除手術,病理報告結果卻證實為橫紋肌肉瘤,這是腎臟橫紋肌肉瘤非常罕見的表現方式。此患者術後並無接受其他輔助治療,於歷經追蹤兩年後仍存活且無復發跡象。 |
英文摘要 | Renal sarcomas are relatively uncommon among all renal malignancies. A renal rhabdomyosarcoma almost always manifests as a renal parenchymal tumor. A 77-year-old female was diagnosed with a right renal pelvic tumor, measuring 2×2×1.8 cm, after the workup for hematuria. She received a nephroureterectomy with bladder cuff excision under the preliminary impression of urothelial cancer. This is a rare presentation of a renal rhabdomyosarcoma. She remained free of recurrence 2 years after receiving only surgical treatment. |
本系統中英文摘要資訊取自各篇刊載內容。