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題 名 | Pathological Fracture as a Manifestation of Extramedullary Blastic Crisis in Chronic Myelogenous Leukemia: Report of One Case=慢性骨髓性白血病以病理性骨折為骨髓外急性轉化之表現:一病例報告 |
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作 者 | 俞欣慧; 盧孟佑; 林東燦; 林凱信; 唐季祿; 周獻堂; | 書刊名 | 臺灣兒科醫學會雜誌 |
卷 期 | 47:3 民95.05-06 |
頁 次 | 頁150-154+165 |
分類號 | 415.635 |
關鍵詞 | 慢性骨髓性白血病; 骨髓外急性轉化; 骨折; Imatinib mesylate; Chronic myelogenous leukemia; Extramedullary blastic crisis; Fracture; |
語 文 | 英文(English) |
英文摘要 | A three-year-old girl with chronic myelogenous leukemia (CML) experienced a pathological fracture of her femur after a demonstrated osteolytic bone lesion. Extramedullary disease (EMD) was diagnosed following the histologic findings of a biopsy of the osteolytic lesion. Frank blast crisis in the bone marrow followed one month later. This was the youngest patient to have been reported in English literature of Philadelphia chromosome positive (Ph+) CML with isolated bony EMD and pathological fracture. Treatment with a tyrosine kinase inhibitor, imatinib mesylate (Gleevec(superscript ®)), in bone marrow accelerated phase of CML was failed to reverse the progression of blastic transformation, neither in the extramedullary bone lesion nor in the bone marrow. |
本系統中英文摘要資訊取自各篇刊載內容。