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題 名 | Panniculitis in Adult Onset Dermatomyositis--Report of Two Cases and Review of the Literature=成人皮肌炎之脂層炎--二病例報告與文獻回顧 |
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作 者 | 林仁心; 朱家瑜; 林瑞宜; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 24:3 民95.09 |
頁 次 | 頁194-200 |
分類號 | 415.762 |
關鍵詞 | 皮肌炎; 脂層炎; Panniculitis; Dermatomyositis; |
語 文 | 英文(English) |
中文摘要 | 對於皮肌炎的病人而言,脂層炎是極為少見的臨床表現,在我們回顧的文獻中,發現只有18個病例報告。雖然在結締組織疾病的病程中原本有時就可以觀察到脂層炎的表現,但是大多數病例是發生於紅斑性狼瘡的病人,只有極少數是發生於皮肌炎的病人。由於文獻中報告的病例數不多,要詳細探討脂層炎發生於皮肌炎病人的臨床意義實有困難。我們在此報告兩個皮肌炎合併脂層炎臨床表現的案例。脂層炎應該被納入皮肌炎的皮膚臨床表現之一。此外,對於原因不明的小葉性脂層炎,我們應該將皮肌炎納入鑑別診斷範圍內。 |
英文摘要 | Panniculitis is an exceedingly rarely reported clinical finding in dermatomyositis (DM) with a total of only 18 cases reported in the literature. Although panniculitis sometimes occurs during the course of connective tissue disease, it has most often been associated with lupus erythematosus rather than dermatomyositis. Because the reported cases are few, it is difficult to know the significance of this association. Here we report two additional cases of DM in whom clinically manifest panniculitis developed during the course of disease. Panniculitis can be a cutaneous features of DM and it may be prudent to include DM in the differential diagnosis of lobular panniculitis. |
本系統中英文摘要資訊取自各篇刊載內容。