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- Delayed Postpartum Hemorrhage--A Rare Clinical Presentation of Thrombotic Thrombocytopenic Purpura-Hemolytic Uremic Syndrome: A Case Report
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題 名 | Delayed Postpartum Hemorrhage--A Rare Clinical Presentation of Thrombotic Thrombocytopenic Purpura-Hemolytic Uremic Syndrome: A Case Report=遲發性產後出血:血栓性血小板減少性紫斑--溶血性尿毒症候群之罕見臨床表現--病例報告 |
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作 者 | 陳渝潔; 陳鴻昇; 沈靜茹; 張慧名; 蔡英美; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 21:11 民94.11 |
頁 次 | 頁532-535 |
分類號 | 417.453 |
關鍵詞 | 遲發性產後出血; 血栓性血小板減少性紫斑; 溶血性尿毒症候群; Delayed postpartum hemorrhage; Thrombotic thrombocytopenic purpura; Hemolytic uremic syndrome; |
語 文 | 英文(English) |
中文摘要 | 在臨床上,血栓性血小板減少性紫斑症和溶血性尿毒症兩者的臨床表現相當的相似,常常被一起稱為血栓性血小板減少性紫斑-溶血性尿毒症候群。這個症候群的發生可能和病毒或細菌的感染、懷孕、惡性腫瘤、某些藥物 (如化學治療藥物) 和自體免疫性疾病等有關。病人臨床的特徵往往包括有溶血性貧血、血小板缺乏、腎機能異常、發燒以及神經疾患等等。女性的發生率高於男性且容易發生於懷孕中或剛生產後。回顧文獻報告,此類疾病極少以延遲性產後出血來表現。本文中,我們報告一位反覆發作延遲性產後出血的產婦,其最後診斷為血栓性血小板減少性紫斑 - 溶血性尿毒症候群之罕見案例。 |
英文摘要 | Thrombotic thrombocytopenic purpura (TTP) and hemolytic uremic syndrome (HUS) are rare and closely related disorders characterized by microangiopathic hemolytic anemia, thrombocytopenia, and renal failure. Many risk factors have been reported including infection, cancer, pregnancy, a variety of drugs (e.g. anticancer drugs), and autoimmune diseases. The incidence of TTP-HUS is higher in females than in males, especially during pregnancy and the immediate postpartum period. Review of the literature reveals that delayed postpartum hemorrhage is a rare clinical presentation of TTP-HUS. We report a case of TTP-HUS with recurrent delayed postpartum hemorrhage and dismal outcome. |
本系統中英文摘要資訊取自各篇刊載內容。