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題 名 | HCV Infection Complicated with Nephrotic Syndrome, Immune Complex Crescentic Glomerulonephritis and Acute Renal Failure: A Case Report=感染HCV男性併發腎病症候群、免疫複合體、半月狀腎絲球腎炎以及急性腎衰竭之一--病例報告 |
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作 者 | 陳宜鈞; 郭美娟; 陳鴻鈞; 賴永勳; 黃尚志; | 書刊名 | The Kaohsiung Journal of Medical Sciences |
卷 期 | 21:10 民94.10 |
頁 次 | 頁470-474 |
分類號 | 415.695 |
關鍵詞 | HCV感染; HCV相關性自體免疫疾病; 腎病症候群; 腎絲球腎炎; 腎衰竭; HCV infection; HCV-associated autoimmune disease; Nephrotic syndrome; Crescentic glomerulonephritis; Renal failure; |
語 文 | 英文(English) |
中文摘要 | 已有廣泛的證據指出 HCV 相關的自體免疫性在一群自體免疫疾病中扮演的角色,但常被忽略。 在此我們提出一位 HCV 感染之男性,表現出腎病症候群、可摸性紫瘢、冷凝球蛋白血症、低補體血症、併發免疫性複合體腎絲球腎炎以及腎衰竭。起初認為只是 HCV 相關性冷凝球蛋白血症腎絲球腎炎;然而,腎臟切片顯示全盤性激奇 (full house)腎絲球腎炎,不禁令人思索:此病的元兇是誰?此外針對臨床醫師無可避免面臨的 “ HCV 相關性自體免疫疾病出現似狼瘡性腎炎之轉換 ”,提出治療之經驗。 |
英文摘要 | There is ample evidence suggesting that hepatitis C virus (HCV)-associated autoimmunity plays a role in a broad spectrum of autoimmune diseases, which are usually overlooked. We report on a case of nephritic syndrome, palpable purpura, cryoglobulinemia, hypocomplementemia, and acute renal failure complicated by immune complex glomerulonephritis (GN). The patient is a 64-year-old man with HCV infection, who was initially considered to present only an HCV-associated cryoglobulinemic GN. However, renal biopsy revealed a “full house” immune complex crescentic GN, which led to our subsequent investigation. The attending clinicians faced what is a common dilemma, where an HCV-associated autoimmune disease inevitably switches to a lupus-like GN. Hence, we also discuss treatment. |
本系統中英文摘要資訊取自各篇刊載內容。