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題 名 | Brain Tumor in Lynch Syndrome: A Case Report=腦瘤於Lynch症侯群之病例報告 |
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作 者 | 張志儒; 李興中; 黃金山; 黃世鴻; | 書刊名 | 中華民國外科醫學會雜誌 |
卷 期 | 33:6 民89.11-12 |
頁 次 | 頁300-303 |
分類號 | 416.291 |
關鍵詞 | 腦瘤; Lynch症侯群; 遺傳性非息肉性大腸直腸癌症候群; Glioblastoma multiforme; Brain neoplasms; Neoplastic syndromes; Hereditary; Lynch syndrome; |
語 文 | 英文(English) |
中文摘要 | Lynch症候群又稱為遺傳性分息肉性大腸直腸症候群。眾所周知的,它常常會發展出大腸以外的癌症。例如:胃、小腸、膽道、腎臟、卵巢以及最常見的子宮內膜癌。原發性腦瘤很少被提出來。我們在此提出一個少見的病例,他是一個有Lynch症候群家族史而罹患多形神經膠母細胞瘤的16歲病人。藉由其臨床位狀、治療過程以及查閱文獻,從而討論原發性腦瘤與Lynch症狀群之間的關係。 |
英文摘要 | Hereditary nonpolyposis colorectal cancer (HNPCC, Lynch syndrome) was originally called the cancer family syndrome. Subdividing the Lynch syndrome into Lynch I (colorectal cancer only) and Lynch II (colorectal and extracolonic tumors) are based on the presence or abscece of extracolonic tumors. Brain tumor is rarely found in Lynch Syndrome. We herein describe a 16-year-old male patient with glioblastoma multiforme who is a son of a proband of cancer family syndrome with an unusual aggregation of colorectal cancer. The possibility of brain tumors as a rare spectrum of neoplasms in cancer family syndrome is discussed. |
本系統中英文摘要資訊取自各篇刊載內容。