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題 名 | Nasal T/NK Cell Lymphoma Associated with Virus Infection in Two Cases of Lethal Midline Granuloma=兩個致命性中線肉芽腫病例:鼻部T/NK細胞淋巴瘤合併Epstein-Barr病毒感染 |
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作 者 | 邱慧嫻; 黃柏翰; 黃秀鈺; 李瑞年; 何宜承; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 18:2 2000.06[民89.06] |
頁 次 | 頁88-94 |
分類號 | 416.871 |
關鍵詞 | 中線肉芽腫; 鼻部T/NK細胞淋巴瘤; Epstein-Barr病毒; Nasal T/NK cell lymphoma; Lethal midline granuloma; Epstein-barr virus; |
語 文 | 英文(English) |
中文摘要 | 鼻部或鼻型T/NK細胞淋巴瘤通常病情惡化快速且預後不良,放射治療對早期的局部病灶可有效控制,但化學治療的反應則不佳,未即時有正確的診斷常導致不當的治療。我們提出兩側鼻部 T/NK細胞淋巴瘤,臨床表現為所謂的致命性中線肉芽腫,病人在臉部的中央有一壞死結痂的潰瘍,周圍有紅的浸潤性病灶。病理切片下有異常淋巴細胞廣泛地浸潤,特別是在血管的周圍。免疫組織化學分析中,CD56及LMP-1階呈陽性,EB病毒的DNA可進一步藉由聚合脢鏈性反應而確定其存在於病灶的皮膚組織中。 |
英文摘要 | Nasal or nasal-type T/NK cell lymphoma often follows an aggressive course and has a poor prognosis. Radiation therapy may provide good local control of the disease in an early stage, while the disease is always resistant to chemotherapy. Failure to recognize this disease often leads to inappropriate management. We report two cases of nasal T/NK cell lymphoma with the unique feature of a crusted necrotic ulcer surrounded by erythematous infiltrative rim at midfacial region, clinically presented as so-called lethal midline granuloma. Histopathologically, the atypical lymphoid cells infiltrated diffusely and displayed angiocentricity. CD56 and latent membrane protein-1 (LMP-1) were identified by immunohistochemistry. The presence of Epstein-Barr virus DNA in the lesional skin was confirmed by polymerase chain reaction. |
本系統中英文摘要資訊取自各篇刊載內容。