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題 名 | A Solitary Laryngeal Neurofibroma in a Pediatric Patient=兒童單發性喉神經纖維瘤 |
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作 者 | 陳益瑋; 方端仁; 李學禹; | 書刊名 | 長庚醫學 |
卷 期 | 27:12 2004.12[民93.12] |
頁 次 | 頁930-933 |
分類號 | 416.894 |
關鍵詞 | 喉神經纖維瘤; 喉頭鏡雷射手術; Laryngeal neurofibroma; Laryngoscopic laser surgery; |
語 文 | 英文(English) |
中文摘要 | 發生於喉部的神經纖維瘤是非常罕見的,它通常會侵犯杓狀軟骨以及杓會厭皺襞。發生於嬰幼兒身上的喉神經纖維瘤常以漸進性的呼吸窘迫來表現,但最終的診斷仍需要在組織學上發現明顯的紡錘型細胞及針對S-100蛋白質的特殊染色來確定。傳統上處理此類腫瘤多以經外頸部路徑手術方式切除。我們在此報告一例4歲的小朋友,利用喉頭鏡及二氧化碳雷射完全切除腫瘤,並經過4年的追蹤而無復發的跡象。對於兒童來說,利用內試鏡手術來處理單發性喉神經纖維瘤,不僅安全有效而且侵犯性小,是可供選擇的一種手術方式。 |
英文摘要 | A neurofibroma of the larynx is a rare disease that usually involves the arytenoids and the aryepiglottic fold. Pediatric patients with a laryngeal neurofibroma often present with progressive dyspnea. A definitive dignosis of a laryngeal neurofibroma is based on the histopathologic demonstration of the characteristic spindle cells, and a positive result in immunohistochemical staining for S-100 protein. Tumpr excision of laryngeal neurofibromas by an external approach was formerly common. We present a case of solitary laryngeal neurofibroma in a 4-year-old child that was completely excised using direct laryngoscopy and a CO2 laser. There has been no recurrence after a follow-up of 4 years. For pediatric patients with an isolated laryngeal neurofibroma, endoscopic surgery provides an alternative approach due to its safety, effectiveness, and minimal invasiveness. |
本系統中英文摘要資訊取自各篇刊載內容。