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相關文獻
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題名 | A Child with Primary Sclerosing Cholangitis Successfully Treated by Liver Transplantation=兒童原發硬化性膽管炎成功以肝臟移植治癒的病例報告 |
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作者 | 陳建翰; 何明志; 李伯皇; 張美惠; 鄭永銘; 倪衍玄; Chen, Chien-han; Ho, Ming-chih; Lee, Po-huang; Chang, Mei-hwei; Jeng, Yung-ming; Ni, Yen-hsuan; |
期刊 | 臺灣兒科醫學會雜誌 |
出版日期 | 20040700、20040800 |
卷期 | 45:4 民93.07-08 |
頁次 | 頁239-241+260 |
分類號 | 417.545 |
語文 | eng |
關鍵詞 | 原發硬化性膽管炎; 兒童; 肝臟移植; Primary sclerosing cholangitis; Children; Liver transplantation; |
中文摘要 | 原發硬化性膽管炎(primary sclerosing cholangitis)主要發生於中年男性,極少見於兒童。而其中須接受肝臟移植者更在少數。在此我們提出一名12歲女童的病例報告,她一開始以發燒、腹痛、疲倦、黃膽、以及脾種大六天爲表現。肝穿刺檢查發現有膽管破壞及門脈區間纖維化的情形。內視鏡遡向膽道胰臟攝影術顯示右側肝內膽管呈現鏈珠狀,而左側膽管消失不見。於是診斷確立爲原發硬化性膽管炎。由於肝功能趨於衰竭,因此對她施行肝臓移植術。術後已追蹤十二個月,至今情況良好,並未再次發生膽管炎或肝硬化的情形。 |
英文摘要 | Primary sclerosing cholangitis (PSC) happens mainly in middle-aged men and is seldom diagnosed in children. Childhood PSC undergoing liver transplantation is rarely reported. Here we present a 12-year-old girl who was admitted with a 6-day history of fever, abdominal pain, fatigue, jaundice, and splenomegaly. Liver histological examination revealed the destroyed bile ducts and bridging fibrosis. Endoscopic retrograde cholangiopancreatography (ERCP) showed beaded appearance of right intrahepatic ducts and absent left intrahepatic ducts. PSC was diagnosed. Because of decompensated liver function, she received a living-related orthotopic liver transplantation (OLT). The post- transplantation course was uneventful during the 12-month follow-up. She experienced neither additional episode of cholangitis nor recurrence of liver cirrhosis after OLT. |
本系統之摘要資訊系依該期刊論文摘要之資訊為主。