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頁籤選單縮合
題 名 | Primary Liposarcoma of the Liver in a 14-Year-Old Child=原發性肝臟脂肪肉瘤於一十四歲兒童 |
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作 者 | 呂佳璘; 謝宗保; 俞志誠; 詹德全; 林志恭; 劉耀基; | 書刊名 | Journal of Medical Sciences |
卷 期 | 23:1 2003.02[民92.02] |
頁 次 | 頁57-59 |
分類號 | 417.5453 |
關鍵詞 | 肝臟脂肪肉瘤; 兒童; Pediatric hepatic tumor; Primary liposarcoma; |
語 文 | 英文(English) |
英文摘要 | Liposarcoma is a rare pediatric hepatic tumor, which usually metastasizes from the retroperitoneum and the extremities. Eight cases of primary liposarcoma of liver had been previously reported, 5 in adults and 3 in children. We present herein the ninth case and discuss this unusual disease entity through a review of the English literature. In Taiwan, this is the first case report. A 14-year-old child complained poor appetite and an abdominal mass. Computed tomographic scans of the abdomen showed a huge well-defined heterogenic hypervascular mass in the right lobe of liver. It was excised and histopathology showed primary hepatic liposarcoma. In particular, preoperative thrombocytosis (platelet counts greater than 720,000/µl) was detected in our patient. The platelet counts dropped rapidly 24 hours after surgery. Fifty days after the operation, the platelet counts were 320,000/µl. To date, there is no experience with primary liposarcoma of the liver complicated with thrombocytosis. Possibly, serial platelet counts may be a clue for detecting relapse of the disease. |
本系統中英文摘要資訊取自各篇刊載內容。