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相關文獻
- Carcinoid Tumor of the Thymus--A Case Report and Review of the Literature
- A Rare, Huge Carcinoid Tumor of the Thymus--A Case Report
- 第一型多發性內分泌腫瘤合併胸腺類癌和異位ACTH分泌症候群
- 胸腺不典型類癌
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- 喉部的非典型類癌--病例報告
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題 名 | A Rare, Huge Carcinoid Tumor of the Thymus--A Case Report=罕見巨大胸腺類癌瘤--病例報告 |
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作 者 | 陳富治; 郭獻源; 陳仁智; 程永隆; 張宏; 禚靖; 于承平; 李世俊; | 書刊名 | 胸腔醫學 |
卷 期 | 19:4 2004.08[民93.08] |
頁 次 | 頁289-294 |
分類號 | 415.935 |
關鍵詞 | 胸腺; 類癌; Thymus; Carcinoid tumor; |
語 文 | 英文(English) |
中文摘要 | 自1972年胸腺類癌瘤才被視為異於胸線的病灶。類癌瘤被分類在APUDomas之中,能製造多種胜?、胺類、激?及前列腺素。胸腺類癌瘤罕見,僅250例在世界文獻報告過。我們這例胸腺類癌瘤(22×16×10cm)大於過去報告的所有病例。利用immunohistochemical studies獲許更正確的鑑別診斷。治療及預後在此報告:治療是包括像腫瘤完全切除術、原發或復發腫瘤的大範圍切除術。放射線療法、輔助性octreotide療法少有成功而化學療法並無益處。儘管有密切追蹤及多方面輔助性療法,胸腺類癌瘤的死亡率仍高。 |
英文摘要 | It was not until 1972 that thymic carcinoids were recognized as distinct lesions and not as variants of thymomas. Carcinoid tumors are classified among the amine precursor uptake and decarboxylation tumors (APUDomas), which have the potential to produce several peptides, amines, kinis, and prostaglandins. Thymic carcinoid tumors are uncommon, and only about 250cases have been reported in the world literature to date. In our case, the thymic carcinoid tumor was bigger (22x16x10cm) than those described before. The use of immunohistochemical studies pemitted a more accurate differentiation and diagnosis of this tumor. The treatment and prognosis are reported herein. Treatment included surgical excision for a complete tumorectomy or debulking of the primary or recurring tumor. Radiotherapy and adjuvant octreotide therapy were used with limited success, and chemotherapy added no benefit. Despite close follow-up and multifaceted adjuvant therapy, the mortality rate for thymic carcinoid tumors remains high. |
本系統中英文摘要資訊取自各篇刊載內容。