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頁籤選單縮合
題 名 | Congenital Short Bowel Syndrome with Malrotation=先天性短腸症候群合併腸扭轉 |
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作 者 | 朱世明; 駱至誠; 周怡宏; 顏如貝; | 書刊名 | 長庚醫學 |
卷 期 | 27:7 民93.07 |
頁 次 | 頁548-550 |
分類號 | 417.547 |
關鍵詞 | 短腸症; 腸扭轉; 靜脈營養; 麩胺; Short bowel synrdome; Malrotation; Parenteral nutrition; Glutamine; |
語 文 | 英文(English) |
中文摘要 | 先天性短腸症候群合併腸扭轉及吸收不良是相當罕見的先天性腸道異常,我們報告一個女嬰病例,她的母六接受規則的產前檢查,但並未發現有羊水過多的現象,出生後是以嚴重的嘔吐、一長遲緩以及吸收不良來表現,同時越來越嚴重;在接受腹腔探查手術後發現她的小腸總長度僅有20公分,同時合併有腸扭轉,我們在施行小腸固手術後給予短期的靜脈營養補充,同時並給予L-glutamine補充在完全水解蛋白配方牛奶中,最後這位女嬰存活下來。目前這位女嬰是15個月大,體重7公斤,發展情況良好。從文獻的探尋中,這個病歷應該是目前所知先天性短腸症的病例中,小腸長度最小的病例。 |
英文摘要 | Congenital short bowel syndrome (SBS) associated with amlroation and malabsorption is a very rare condition. We report on an infant girl with congenital SBS associated with malrotation and malabsorption. No polyhydraminos was noted during the regular prenatal examination. Protracted postnatal postprandial vomiting with progressive failure to thrive was noted. A laparotomy showed the small bowel was only about 20 cm in length. She eventually survived with short-term parenteral nutrition and use of oral L-glutamine supple-mentation. To our knowledge, this might be the shortest length of bowel loop ever reported. Currently, she is 15 months of age with a body weight of about 7 kg and good development. |
本系統中英文摘要資訊取自各篇刊載內容。