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頁籤選單縮合
題 名 | Critical Cardiac Disease in the Newborn=新生兒之重症心臟病 |
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作 者 | 邱曉郁; 蘇百弘; 蔡志清; 林宗文; 林鴻志; 張正成; | 書刊名 | Clinical Neonatology |
卷 期 | 11:1 2004.06[民93.06] |
頁 次 | 頁29-32 |
分類號 | 417.5223 |
關鍵詞 | 新生兒; 心臟病; Critical cardiac disease; Newborn; |
語 文 | 英文(English) |
英文摘要 | A retrospective chart review study was conducted at China Medical University Hospital, Taichung, Taiwan to analyze critical cardiac disease in the newborn. Ninety-five infants with a final diagnosis of congenital heart disease (CHD), including 41 (43%) males and 54 (57%) females admitted to neonatal intensive care unit (NICU) from January 1997 to December 2002, were enrolled. The mean gestational age was 37.9±2.2 wk, the mean birth weight was 2844±728 g, and 23 (24.2%) were premature. Twentynine (30.5%) were inborn, 66 (69.5%) were outborn, and only 9 (9.5%) infants had a prenatal diagnosis. Based on the echocardiographic results, we found 3 (3.2%) infants with double-outlet right ventricle (DORV), 7 (7.4%) with Ebstein’s anomaly, 2 (2.1%) with endocardial cushion defect, 20 (21%) with pulmonary stenosis, 10 (10.5%) with pulmonary atresia, 10 (10.5%) with transposition of the great arteries (TGA), 15 (15.8%) with total anomalous pulmonary venous return (TAPVR), 14 (14.7%) with coarctation of the aorta (COA), 10 (10.5%) with tetralogy of Fallot, and 4 (4.2%) with hypoplastic left heart syndrome. Among the 95 cases there were 9 infants whose initial diagnosis were not CHD, including 4 persistent pulmonary hypertension of the newborn (PPHN) complicated with meconium aspiration syndrome (final diagnosis (fd): 3 TAPVR and 1 with COA), 2 sepsis (fd:1 TGA and 1 COA), 1 asphyxia (fd: TGA), 1 pneumonia (fd: DORV), and 1 inborn error of metabolism (fd: TAPVR). The average hours from admission to a final diagnosis of CHD in 86 infants with and in the 9 infants without an initial diagnosis of CHD were 12.5±2.8 and 74.3±52.9, respectively. Fiftyeight (61%) infants underwent corrective surgery and 22 (37.9%) expired after the operation. The mortality rates of infants with and without an initial diagnosis of CHD were 43% (37/86) and 55.5% (5/9), respectively. The overall mortality rate was 44% (42/95). In newborn, cyanosis due to heart disease must be differentiated from pulmonary problems, sepsis, or PPHN. An initial diagnosis of PPHN is the most common cause of delayed diagnosis of CHD. |
本系統中英文摘要資訊取自各篇刊載內容。