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題 名 | 以急性甲溝炎為先驅症狀的天疱瘡:病例報告及文獻回顧=Pemphigus Vulgaris Heralded by Acute Paronychia: A Case Report and Review of the Literature |
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作 者 | 李華恩; 翁雯柔; 李美青; 洪宏翔; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 22:1 2004.03[民93.03] |
頁 次 | 頁41-45 |
分類號 | 415.765 |
關鍵詞 | 急性甲溝炎; 天疱瘡; Acute paronychia; Pemphigus vulgaris; |
語 文 | 中文(Chinese) |
中文摘要 | 急性甲溝炎,也就是指甲周圍組織的化膿性發炎,過去很少被報告和天疱瘡有關。我們在此報告一個少見的病例:一個四十八歲的女性天疱瘡病人,發生多次侵犯多隻手指、腳趾的急性甲溝炎;而不易控制的甲溝炎往往導致後續皮膚病灶的惡化。於甲溝(paronychium)所做的皮膚切片顯示有基底層上的表皮棘層鬆解;同一部位的直接免疫螢光試驗則有immunoglobulin (Ig) G及C3在細胞間隙沉積。使用全身性類固醇合併azathioprine治療,不但可抑制皮膚黏膜的病灶,也有效地治療了甲溝炎。我們認為在天疱瘡的病人身上發生急性甲溝炎,需要鑑別其原因有可能是疾病本身的一種表現,而非感染所造成的。 |
英文摘要 | Acute paronychia, presenting as abscess formation involving the paronychium of the nails, is thought to be an uncommon feature of pemphigus vulgaris (PV). We report a patient with PV who developed acute paronychia of multiple fingernails and toenails, that precede to the exacerbation of other mucocutaneous lesions. A biopsy specimen of the paronychium of the finger revealed suprabasal acantholysis with pustule formation. Direct immunofluorescence study of the same lesion showed intercellular deposition of immunoglobulin (Ig) G and C3. Systemic corticosteroids and azathioprine were effective in treating both the nail disease and mucocutaneous lesions. We concluded that in patients with PV, acute paronychia could be a manifestation of the disease per se, rather than an infectious process. |
本系統中英文摘要資訊取自各篇刊載內容。