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相關文獻
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題 名 | Calciphylaxis in a Continuous Ambulatory Peritoneal Dialysis Patient After Graft Failure of Cadaveric Kidney Transplantation=鈣過敏症在一屍腎移植失敗接受連續性腹模透析病人之病例報告 |
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作 者 | 王碧華; 朱柏齡; 吳家兆; 林裕峰; | 書刊名 | 臺灣腎臟醫學會雜誌 |
卷 期 | 15:2 2001.06[民90.06] |
頁 次 | 頁77-80+93 |
分類號 | 415.815 |
關鍵詞 | 尿毒性動脈鈣化病變; 鈣過敏症; 腎衰竭; 缺氧性組織壞死; 副甲狀腺亢進症; Calcific uremic arteriopathy; Calciphylaxis; Renal failure; Ischemic tissue necrosis; Hyperparathyroidism; |
語 文 | 英文(English) |
中文摘要 | 尿毒性動脈鈣化病變(鈣過敏症)是一少見且致命之症病,主要發生於未期腎衰接透析治療或換腎病人,症病主要表現為突發性疼痛、缺氧之皮膚病變而漸成壞死,導致不癒合之潰瘍或壞疽。早期診斷是極重要的,因為次發性局部或系統性之感染,若無即時且適當之治療,會導致敗血症和死亡。我們報告一個屍腎移植失敗後接受連續性腹莫透析之男性病患,發生嚴重的高血磷症,副甲狀腺亢進症及鈣過敏症,他的皮膚症灶起先是網狀青斑,之後進展至左側第四腳指疼痛壞死而至接受膝下截肢。治療上以低鈣透析液進行密集性血液透析合併口服給予氫氧化鋁磷結合劑,之後再給予口服維他命D,治療後血清副甲狀腺濃度回復側相對性正常範圍內,然而截肢處之傷口無法完全癒合,病患終致亡於敗血症。我們也回顧鈣過敏症致病機轉及治療之相關文獻。 |
英文摘要 | Calcific uremic arteriopathy (Calciphylaxis) is a rare and life-threatening disorder, occurring mainly in patients with end-stage renal disease (ESRD) undergoing dialysis or with a renal transplant. The disease is manifested by the abrupt onset of painful ischemic skin lesions that become necrotic , leading to non-healing ulcers and/or gangrene. Early diagnosis may be important because secondary local and systemic infection may supervene and, without timely and appropriate intervention, the disease often leads to sepsis and death. We describe a man with ESRD receiving continuous ambulatory peritoneal dialysis (CAPD) after cadaveric kidney transplantation failure. He developed calciphylaxis with a setting of severe hyperparathyroidism (HPT) and hyperphosphatemia. His skin lesions appeared initially as livedo reticulosis and progressed to painful necrosis of the left 4th toe for which he underwent below knee amputation. He received intensive hemodialysis with low calcium dialysate associated with oral aluminum hydroxide phosphate binder followed by oral calcitriol pulse therapy. The serum intact parathyroid hormone (iPTH) level returned to the normal range. However, the wound in amputation leg did not heal completely which ultimately caused the patient to die. |
本系統中英文摘要資訊取自各篇刊載內容。