查詢結果分析
來源資料
頁籤選單縮合
題 名 | Rudimentary Meningocele of the Scalp=頭皮上痕跡性腦脊髓膜膨出 |
---|---|
作 者 | 盧靜怡; 張雅菁; 賴昌和; 郭承統; 洪宏翔; | 書刊名 | 中華皮膚科醫學雜誌 |
卷 期 | 21:4 2003.12[民92.12] |
頁 次 | 頁394-401 |
分類號 | 415.78 |
關鍵詞 | 痕跡性腦脊髓膜膨出; 原發性皮膚腦膜瘤; Epithelial membrane antigen; EMA; Primary cutaneous meningioma; Rudimentary meningocele; Vimentin; |
語 文 | 英文(English) |
中文摘要 | 痕跡性腦脊髓膜膨出是一種原發性皮膚腦膜瘤的變異型,是罕見的胚胎學上的畸形。我們研究五個病例,他們自出生即在枕部發現有一塊禿髮的病灶。在腦部電腦斷層或超音波下,沒有發現骨骼缺陷或與顱內相通部份。病理下,主要變化集中在皮下組織,可以看到一縷縷嵌於緻密膠原組織的腦脊髓膜細胞。這些細胞在免疫染色下可表現vimentin及上皮膜抗原(epithelial membrane antigen, EMA),但缺乏細胞角質,S-100蛋白,平滑肌肌動蛋白及內皮細胞標記。我們提出此罕見疾病,並且回顧相關文獻。 |
英文摘要 | Rudimentary meningocele, a variant of primary cutaneous meningioma, is a rare embryologic malformation with meningeal tissue occurring in the skin. This work studied five cases of this condition. All five cases were congenital and presented as alopecic lesions on the occipital area. No underlying bony defect or communication to the intracranial compartment was detected by brain computed tomography (CT) or echoencephalogram. Histologically, the major changes were mostly concentrated in the subcutis, where strands of meningothelial cells were embedded in dense collagenous tissue. The meningothelial cells were immunopositive for vimentin and epithelial membrane antigen and lacked cytokeratin, S-l00 protein, smooth muscle actin and endothelial markers. The related literature also was reviewed. |
本系統中英文摘要資訊取自各篇刊載內容。